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Propionyl CoA Carboxylase, alpha Polypeptide 产品

(Propionyl CoA Carboxylase, alpha Polypeptide (PCCA))

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The protein encoded by this gene is the alpha subunit of the heterodimeric mitochondrial enzyme Propionyl-CoA carboxylase. PCCA encodes the biotin-binding region of this enzyme. Mutations in either PCCA or PCCB (encoding the beta subunit) lead to an enzyme deficiency resulting in propionic acidemia. Multiple transcript variants encoding different isoforms have been found for this gene.[provided by RefSeq, May 2010].

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Featured Propionyl CoA Carboxylase, alpha Polypeptide Categories

Propionyl CoA Carboxylase, alpha Polypeptide 抗体

High quality antibodies with extensive validation data.

Propionyl CoA Carboxylase, alpha Polypeptide 蛋白

Proteins for various applications incl. WB, ELISA, IF etc.

Recommended Propionyl CoA Carboxylase, alpha Polypeptide 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human, Rat
Application WB, IHC (p)
Validations
  • (7)
Cat. No. ABIN656262
Quantity 400 μL
Datasheet Datasheet
Reactivity Human
Application WB
Validations
  • (2)
  • (3)
Cat. No. ABIN518660
Quantity 50 μg
Datasheet Datasheet
Reactivity Human
Application WB, ELISA, IHC
Validations
  • (3)
Cat. No. ABIN7164812
Quantity 100 μg
Datasheet Datasheet

Recommended Propionyl CoA Carboxylase, alpha Polypeptide ELISA试剂盒

Product
Reactivity
Analytical Method
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Analytical Method
Validations
Cat. No. ABIN419368
Quantity 96 tests
Datasheet Datasheet
Reactivity Human
Analytical Method Quantitative Sandwich ELISA
Validations
Cat. No. ABIN6231717
Quantity 96 tests
Datasheet Datasheet

Recommended Propionyl CoA Carboxylase, alpha Polypeptide 蛋白

Product
Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Source Wheat germ
Validations
  • (1)
Cat. No. ABIN1314137
Quantity 10 μg
Datasheet Datasheet
Reactivity Mouse
Source Escherichia coli (E. coli)
Validations
Cat. No. ABIN7423447
Quantity 100 μg
Datasheet Datasheet
Reactivity Human
Source Escherichia coli (E. coli)
Validations
Cat. No. ABIN7419790
Quantity 100 μg
Datasheet Datasheet

Latest Publications for our Propionyl CoA Carboxylase, alpha Polypeptide Products

Majtan, Kraus: "Folding and activity of mutant cystathionine ?-synthase depends on the position and nature of the purification tag: characterization of the R266K CBS mutant." in: Protein expression and purification, Vol. 82, Issue 2, pp. 317-24, (2012) (PubMed).

Rincón, Aguado, Desviat, Sánchez-Alcudia, Ugarte, Pérez: "Propionic and methylmalonic acidemia: antisense therapeutics for intronic variations causing aberrantly spliced messenger RNA." in: American journal of human genetics, Vol. 81, Issue 6, pp. 1262-70, (2011) (PubMed).

Chandler, Chandrasekaran, Carrillo-Carrasco, Senac, Hofherr, Barry, Venditti: "Adeno-associated virus serotype 8 gene transfer rescues a neonatal lethal murine model of propionic acidemia." in: Human gene therapy, Vol. 22, Issue 4, pp. 477-81, (2011) (PubMed).

Synonyms and alternative names related to Propionyl CoA Carboxylase, alpha Polypeptide

propionyl-CoA carboxylase alpha subunit (PCCA), propionyl-CoA carboxylase alpha subunit (Pcca), propionyl-COA carboxylase alpha chain, mitochondrial (BMEI0800), propionyl-CoA carboxylase alpha chain (pccA), propionyl-CoA carboxylase alpha chain (NRI_0781), zinc finger CCCH-type containing 13 (zc3h13), propionyl-Coenzyme A carboxylase, alpha polypeptide (Pcca), propionyl CoA carboxylase, alpha polypeptide (pcca), propionyl-CoA carboxylase alpha subunit L homeolog (pcca.L), C79630, pcca, wu:fb92g02, zgc:66359, zgc:100925

Protein level used designations for Propionyl CoA Carboxylase, alpha Polypeptide

  • PCCase alpha subunit
  • pccA complementation group
  • propanoyl-CoA:carbon dioxide ligase alpha subunit
  • propionyl Coenzyme A carboxylase, alpha polypeptide
  • propionyl-CoA carboxylase alpha chain, mitochondrial
  • PCCase subunit alpha
  • Propionyl Coenzyme A carboxylase alpha polypeptide
  • propanoyl-CoA:carbon dioxide ligase subunit alpha
  • propionyl-coenzyme A carboxylase, alpha polypeptide
  • propionyl-COA carboxylase alpha chain, mitochondrial
  • propionyl-CoA carboxylase alpha chain
  • zinc finger CCCH domain-containing protein 13
  • propionyl-Coenzyme A carboxylase, alpha polypeptide
  • propionyl CoA-carboxylase alpha
  • fb92g02
  • propionyl CoA carboxylase, alpha polypeptide
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