HMBS 产品
(Hydroxymethylbilane Synthase (HMBS))
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This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described. [provided by RefSeq, Jul 2008].
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Featured HMBS Categories
HMBS 抗体
High quality antibodies with extensive validation data.
HMBS ELISA试剂盒
Reliable ELISA kits for a wide range of species.
HMBS 蛋白
Proteins for various applications incl. WB, ELISA, IF etc.
Recommended HMBS 抗体
Product
Reactivity
Application
Validations
Cat. No.
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Datasheet
Reactivity
Human
Application
WB, ELISA, IHC, IF
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- (4)
Cat. No.
ABIN7163904
Quantity
100 μg
Datasheet
Datasheet
Reactivity
Human
Application
WB, IF
Validations
- (1)
- (2)
Cat. No.
ABIN516532
Quantity
100 μg
Datasheet
Datasheet
Reactivity
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Application
WB, ELISA
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- (3)
Cat. No.
ABIN516533
Quantity
100 μg
Datasheet
Datasheet
Recommended HMBS ELISA试剂盒
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Reactivity
Analytical Method
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Cat. No.
Quantity
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Reactivity
Human
Analytical Method
Quantitative Sandwich ELISA
Validations
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Cat. No.
ABIN6956629
Quantity
96 tests
Datasheet
Datasheet
Reactivity
Mouse
Analytical Method
Quantitative Sandwich ELISA
Validations
Cat. No.
ABIN6204971
Quantity
96 tests
Datasheet
Datasheet
Reactivity
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Analytical Method
Quantitative Sandwich ELISA
Validations
Cat. No.
ABIN5592154
Quantity
96 tests
Datasheet
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Recommended HMBS 蛋白
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Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity
Human
Source
Escherichia coli (E. coli)
Validations
- (1)
Cat. No.
ABIN7123381
Quantity
50 μg
Datasheet
Datasheet
Reactivity
Human
Source
Wheat germ
Validations
- (1)
Cat. No.
ABIN1306784
Quantity
10 μg
Datasheet
Datasheet
Reactivity
Human
Source
Human Cells
Validations
Cat. No.
ABIN7318923
Quantity
50 μg
Datasheet
Datasheet
Latest Publications for our HMBS Products
: "Systemic messenger RNA as an etiological treatment for acute intermittent porphyria. ..." in: Nature medicine, Vol. 24, Issue 12, pp. 1899-1909, (2018) (PubMed).: "Vitamin D3 enhances the apoptotic response of epithelial tumors to aminolevulinate-based photodynamic therapy." in: Cancer research, Vol. 71, Issue 18, pp. 6040-50, (2011) (PubMed).
: "Acute intermittent porphyria with peripheral neuropathy: a follow-up study after hematin treatment." in: Journal of the neurological sciences, Vol. 260, Issue 1-2, pp. 231-5, (2007) (PubMed).
Synonyms and alternative names related to HMBS
hydroxymethylbilane synthase (HMBS), hydroxymethylbilane synthase (Hmbs), hydroxymethylbilane synthase (hmbs), hydroxymethylbilane synthase S homeolog (hmbs.2.S), hydroxymethylbilane synthase L homeolog (hmbs.L), hydroxymethylbilane synthase (CNC02250), hydroxymethylbilane synthase (predicted) (hem3), hydroxymethylbilane synthase (hemC), Hydroxymethylbilane synthase (Trad_0335), hydroxymethylbilane synthase (Plabr_2100), hydroxymethylbilane synthase (Sgly_3113), hydroxymethylbilane synthase (SMLT_RS19660), hydroxymethylbilane synthase (PMI_RS16580), hydroxymethylbilane synthase a (hmbsa), hydroxymethylbilane synthase, b (hmbsb), DDBDRAFT_0186148, DDBDRAFT_0231417, DDB_0186148, DDB_0231417, hemC, Hmbs, hmbs, hmbsl, id:ibd5004, im:7140060, NV50236, PBG-D, pbg-d, PBGD, pbgd, PORC, SPAC806.01, T25658, UPS, ups, Ups, URO-S, Uros1, zgc:64128, zgc:110690Protein level used designations for HMBS
- porphobilinogen deaminase
- porphyria, acute; Chester type
- pre-uroporphyrinogen synthase
- uroporphyrinogen I synthase
- uroporphyrinogen I synthetase
- alternative name: porphobilinogen deaminase
- hydroxymethylbilane synthase
- Hydroxymethylbilane synthase
- PBG-D
- porphobilinogen deaminase-like
- hydroxymethylbilane synthase, b
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