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GBE1 抗体

(Glucan (1,4-alpha-), Branching Enzyme 1 (GBE1))
The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease). [provided by RefSeq, Jul 2008].
GBE1 抗体 GBE1 抗体 GBE1 抗体 (ABIN1498396)

GBE1 适用: 人 WB, IHC, IP, FACS, IHC (p) 宿主: 小鼠 Monoclonal 5B7 unconjugated

GBE1 抗体 GBE1 抗体 GBE1 抗体 (ABIN1498395)

GBE1 适用: 人 WB, IF, IP, FACS 宿主: 小鼠 Monoclonal 4D9 unconjugated

GBE1 抗体 GBE1 抗体 GBE1 抗体 (ABIN2721750)

GBE1 适用: 人 WB, IHC, IF, IP, FACS 宿主: 小鼠 Monoclonal 1D11 unconjugated

GBE1 抗体 by 适用

Find GBE1 抗体 for a variety of species such as anti-Human GBE1, anti-Mouse GBE1, anti-Rat GBE1. The species listed below are among those available. Click on a link to go to the corresponding products.

GBE1 抗体 by 应用范围

Find GBE1 抗体 validated for a specific application such as WB, ELISA, IF, IF (cc). Some of the available applications are listed below. Click on a link to go to the corresponding products.

GBE1 抗体 by 抗体来源

Find GBE1 抗体 with a specific 抗体来源. The 抗体来源 listed below are among those available. Click on a link to go to the corresponding products.

GBE1 抗体 by 抗原表位

Find GBE1 抗体 with a specific epitope. The epitopes listed below are among those available. Click on a link to go to the corresponding products.

GBE1 抗体 by 克隆形成能力

Find available monoclonal or polyclonal GBE1 抗体. Click on a link to go to the corresponding products.

GBE1 抗体 by 克隆

Find GBE1 抗体 with a specific 克隆. The 克隆 listed below are among those available. Click on a link to go to the corresponding products.

GBE1 抗体 by 标记

Find GBE1 抗体 with a specific conjugate such as Biotin, FITC, HRP. The conjugates listed below are among those available. Click on a link to go to the corresponding products.

Popular GBE1 抗体

Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity Human
Application WB, IHC, IP, FACS, IHC (p)
Validations
  • (9)
Cat. No. ABIN1498396
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, IF, IP, FACS
Validations
  • (4)
Cat. No. ABIN1498395
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, IHC, IF, IP, FACS
Validations
  • (2)
  • (3)
Cat. No. ABIN2721750
Quantity 0.1 mL
Datasheet Datasheet
Reactivity Human
Application WB, ELISA, IHC
Validations
  • (2)
Cat. No. ABIN7142066
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, ELISA
Validations
  • (2)
  • (1)
Cat. No. ABIN561010
Quantity 50 μL
Datasheet Datasheet
Reactivity Human
Application WB, IP
Validations
  • (2)
Cat. No. ABIN947904
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB
Validations
  • (2)
Cat. No. ABIN515961
Quantity 50 μg
Datasheet Datasheet
Reactivity Human, Mouse
Application WB, IF
Validations
  • (3)
Cat. No. ABIN653459
Quantity 400 μL
Datasheet Datasheet
Reactivity Human, Mouse
Application WB, IF, EIA
Validations
  • (3)
Cat. No. ABIN952469
Quantity 0.4 mL
Datasheet Datasheet
Reactivity Human
Application WB, ELISA, IF (cc), IF (p), ICC, IHC (p), IHC (fro)
Validations
Cat. No. ABIN1713806
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, ELISA, IHC (p), IHC (fro)
Validations
Cat. No. ABIN1700304
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, IF (cc), IF (p)
Validations
Cat. No. ABIN2813610
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, IF (cc), IF (p)
Validations
Cat. No. ABIN1696680
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, IF (cc), IF (p)
Validations
Cat. No. ABIN1694852
Quantity 100 μL
Datasheet Datasheet
Reactivity Human
Application WB, IF (cc), IF (p)
Validations
Cat. No. ABIN1693037
Quantity 100 μL
Datasheet Datasheet

Latest Publications for our GBE1 抗体

Colombo, Pagliarani, Testolin, Salsano, Napoli, Bordoni, Salani, DAdda, Morandi, Farina, Magri, Riva, Prelle, Sciacco, Comi, Moggio: "Adult polyglucosan body disease: clinical and histological heterogeneity of a large Italian family." in: Neuromuscular disorders : NMD, Vol. 25, Issue 5, pp. 423-8, (2015) (PubMed).

Irimia, Tagliabracci, Meyer, Segvich, DePaoli-Roach, Roach: "Muscle glycogen remodeling and glycogen phosphate metabolism following exhaustive exercise of wild type and laforin knockout mice." in: The Journal of biological chemistry, (2015) (PubMed).

Orhan Akman, Emmanuele, Kurt, Kurt, Sheiko, DiMauro, Craigen: "A novel mouse model that recapitulates adult-onset glycogenosis type 4." in: Human molecular genetics, Vol. 24, Issue 23, pp. 6801-10, (2015) (PubMed).

Kakhlon, Glickstein, Feinstein, Liu, Baba, Terashima, Akman, Dimauro, Lossos: "Polyglucosan neurotoxicity caused by glycogen branching enzyme deficiency can be reversed by inhibition of glycogen synthase." in: Journal of neurochemistry, Vol. 127, Issue 1, pp. 101-13, (2013) (PubMed).

Akman, Sheiko, Tay, Finegold, Dimauro, Craigen: "Generation of a novel mouse model that recapitulates early and adult onset glycogenosis type IV." in: Human molecular genetics, Vol. 20, Issue 22, pp. 4430-9, (2011) (PubMed).

Aliases for GBE1 抗体

1,4-alpha-glucan branching protein GlgB (glgB) 抗体
1,4-alpha-glucan branching protein (glgB) 抗体
glycogen branching protein (ECs4277) 抗体
glycogen branching protein (glgB) 抗体
glycogen branching enzyme (glgB) 抗体
1,4-alpha-glucan-branching protein (SCO7332) 抗体
glycogen branching enzyme; BE; 1,4-alpha-D-glucan:1,4-alpha-D-glucan 6-glucosyl-transferase (glgB) 抗体
glycogen branching enzyme (Synpcc7942_1085) 抗体
glycogen branching enzyme (AZC_4116) 抗体
glycogen branching enzyme (Sros_8169) 抗体
glycogen branching enzyme (Despr_0975) 抗体
1,4-alpha-glucan branching enzyme 1 (GBE1) 抗体
glucan (1,4-alpha-), branching enzyme 1 (Gbe1) 抗体
1,4-alpha-glucan branching enzyme 1 (Gbe1) 抗体
2310045H19Rik 抗体
2810426P10Rik 抗体
APBD 抗体
D16Ertd536e 抗体
GBE 抗体
glgBII 抗体
GSD4 抗体
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