GBE1 产品
(Glucan (1,4-alpha-), Branching Enzyme 1 (GBE1))
Categories
The protein encoded by this gene is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease). [provided by RefSeq, Jul 2008].
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Featured GBE1 Categories
GBE1 抗体
High quality antibodies with extensive validation data.
GBE1 ELISA试剂盒
Reliable ELISA kits for a wide range of species.
GBE1 蛋白
Proteins for various applications incl. WB, ELISA, IF etc.
Recommended GBE1 抗体
Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity
Human
Application
WB, IHC, IP, FACS, IHC (p)
Validations
- (9)
Cat. No.
ABIN1498396
Quantity
100 μL
Datasheet
Datasheet
Reactivity
Human
Application
WB, IF, IP, FACS
Validations
- (4)
Cat. No.
ABIN1498395
Quantity
100 μL
Datasheet
Datasheet
Reactivity
Human
Application
WB, IHC, IF, IP, FACS
Validations
- (2)
- (3)
Cat. No.
ABIN2721750
Quantity
0.1 mL
Datasheet
Datasheet
Recommended GBE1 ELISA试剂盒
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Reactivity
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Cat. No.
Quantity
Datasheet
Reactivity
Human
Analytical Method
Validations
Cat. No.
ABIN1118626
Quantity
96 tests
Datasheet
Datasheet
Reactivity
Mouse
Analytical Method
Validations
Cat. No.
ABIN1118627
Quantity
96 tests
Datasheet
Datasheet
Reactivity
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Analytical Method
Quantitative Competition ELISA
Validations
Cat. No.
ABIN1742631
Quantity
96 tests
Datasheet
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Recommended GBE1 蛋白
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Reactivity
Source
Validations
Cat. No.
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Datasheet
Reactivity
Human
Source
Wheat germ
Validations
- (1)
Cat. No.
ABIN1354871
Quantity
10 μg
Datasheet
Datasheet
Reactivity
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Source
Wheat germ
Validations
- (1)
Cat. No.
ABIN1354873
Quantity
10 μg
Datasheet
Datasheet
Reactivity
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Source
HEK-293 Cells
Validations
- (1)
Cat. No.
ABIN2721752
Quantity
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Datasheet
Datasheet
Latest Publications for our GBE1 Products
: "Adult polyglucosan body disease: clinical and histological heterogeneity of a large Italian family." in: Neuromuscular disorders : NMD, Vol. 25, Issue 5, pp. 423-8, (2015) (PubMed).: "Muscle glycogen remodeling and glycogen phosphate metabolism following exhaustive exercise of wild type and laforin knockout mice." in: The Journal of biological chemistry, (2015) (PubMed).
: "A novel mouse model that recapitulates adult-onset glycogenosis type 4." in: Human molecular genetics, Vol. 24, Issue 23, pp. 6801-10, (2015) (PubMed).
: "Polyglucosan neurotoxicity caused by glycogen branching enzyme deficiency can be reversed by inhibition of glycogen synthase." in: Journal of neurochemistry, Vol. 127, Issue 1, pp. 101-13, (2013) (PubMed).
: "Generation of a novel mouse model that recapitulates early and adult onset glycogenosis type IV." in: Human molecular genetics, Vol. 20, Issue 22, pp. 4430-9, (2011) (PubMed).
Synonyms and alternative names related to GBE1
1,4-alpha-glucan branching protein GlgB (glgB), 1,4-alpha-glucan branching protein (glgB), glycogen branching protein (ECs4277), glycogen branching protein (glgB), glycogen branching enzyme (glgB), 1,4-alpha-glucan-branching protein (SCO7332), glycogen branching enzyme; BE; 1,4-alpha-D-glucan:1,4-alpha-D-glucan 6-glucosyl-transferase (glgB), glycogen branching enzyme (Synpcc7942_1085), glycogen branching enzyme (AZC_4116), glycogen branching enzyme (Sros_8169), glycogen branching enzyme (Despr_0975), 1,4-alpha-glucan branching enzyme 1 (GBE1), glucan (1,4-alpha-), branching enzyme 1 (Gbe1), 1,4-alpha-glucan branching enzyme 1 (Gbe1), 2310045H19Rik, 2810426P10Rik, APBD, D16Ertd536e, GBE, glgBII, GSD4Protein level used designations for GBE1
- glycogen branching enzyme
- 1,4-alpha-glucan-branching enzyme
- amylo-(1,4 to 1,6) transglucosidase
- amylo-(1,4 to 1,6) transglycosylase
- brancher enzyme
- glycogen-branching enzyme
- glucan (1,4-alpha-), branching enzyme 1 (glycogen branching enzyme, Andersen disease, glycogen storage disease type IV)
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