FH 产品
(Fumarate Hydratase (FH))
Categories
The protein encoded by this gene is an enzymatic component of the tricarboxylic acid (TCA) cycle, or Krebs cycle, and catalyzes the formation of L-malate from fumarate. It exists in both a cytosolic form and an N-terminal extended form, differing only in the translation start site used. The N-terminal extended form is targeted to the mitochondrion, where the removal of the extension generates the same form as in the cytoplasm. It is similar to some thermostable class II fumarases and functions as a homotetramer. Mutations in this gene can cause fumarase deficiency and lead to progressive encephalopathy. [provided by RefSeq, Jul 2008].
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Featured FH Categories
FH 抗体
High quality antibodies with extensive validation data.
FH ELISA试剂盒
Reliable ELISA kits for a wide range of species.
FH 蛋白
Proteins for various applications incl. WB, ELISA, IF etc.
Recommended FH 抗体
Product
Reactivity
Application
Validations
Cat. No.
Quantity
Datasheet
Reactivity
Human
Application
WB, IHC, IP, ICC
Validations
- (6)
Cat. No.
ABIN7444424
Quantity
100 μL
Datasheet
Datasheet
Reactivity
Dog, Human, Rat
Application
WB, IHC, IF, IHC (p), FACS
Validations
- (7)
Cat. No.
ABIN1498267
Quantity
100 μL
Datasheet
Datasheet
Reactivity
Human
Application
WB, IF, IHC (p), ICC
Validations
- (1)
- (5)
Cat. No.
ABIN2856710
Quantity
100 μL
Datasheet
Datasheet
Recommended FH ELISA试剂盒
Product
Reactivity
Analytical Method
Validations
Cat. No.
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Datasheet
Reactivity
Human
Analytical Method
Quantitative Sandwich ELISA
Validations
- (1)
Cat. No.
ABIN6966911
Quantity
96 tests
Datasheet
Datasheet
Reactivity
Mouse
Analytical Method
Validations
Cat. No.
ABIN1133786
Quantity
96 tests
Datasheet
Datasheet
Reactivity
Rat
Analytical Method
Validations
Cat. No.
ABIN1133788
Quantity
96 tests
Datasheet
Datasheet
Recommended FH 蛋白
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Reactivity
Source
Validations
Cat. No.
Quantity
Datasheet
Reactivity
Human
Source
Escherichia coli (E. coli)
Validations
- (1)
Cat. No.
ABIN666730
Quantity
100 μg
Datasheet
Datasheet
Reactivity
Human
Source
Wheat germ
Validations
- (1)
Cat. No.
ABIN1354068
Quantity
10 μg
Datasheet
Datasheet
Reactivity
Human
Source
Escherichia coli (E. coli)
Validations
Cat. No.
ABIN7418329
Quantity
100 μg
Datasheet
Datasheet
Latest Publications for our FH Products
: "Combined effects of FH (E404D) and ACOX2 (R409H) cause metabolic defects in primary cardiac malignant tumor." in: Cell death discovery, Vol. 4, pp. 18, (2018) (PubMed).: "Fumarase-deficient Uterine Leiomyomas: An Immunohistochemical, Molecular Genetic, and Clinicopathologic Study of 86 Cases." in: The American journal of surgical pathology, Vol. 40, Issue 12, pp. 1661-1669, (2017) (PubMed).
: "Insulin Resistance in Human iPS Cells Reduces Mitochondrial Size and Function." in: Scientific reports, Vol. 6, pp. 22788, (2016) (PubMed).
: "Differential proteomic expression of human placenta and fetal development following e-waste lead and cadmium exposure in utero." in: The Science of the total environment, Vol. 550, pp. 1163-1170, (2016) (PubMed).
: "Mitochondrial membrane assembly of TMEM70 protein." in: Mitochondrion, Vol. 15, pp. 1-9, (2014) (PubMed).
: "High molecular weight forms of mammalian respiratory chain complex II." in: PLoS ONE, Vol. 8, Issue 8, pp. e71869, (2013) (PubMed).
: "Alterations in the mitochondrial proteome of neuroblastoma cells in response to complex 1 inhibition." in: Journal of proteome research, Vol. 10, Issue 4, pp. 1974-86, (2011) (PubMed).
: "Targeted inactivation of fh1 causes proliferative renal cyst development and activation of the hypoxia pathway." in: Cancer cell, Vol. 11, Issue 4, pp. 311-9, (2007) (PubMed).
Synonyms and alternative names related to FH
fumarate hydratase (FH), fumarate hydratase (fumH), fumarate hydratase (Fh), fumarate hydratase (fh), fumarate hydratase 1 (Fh1), DDBDRAFT_0205237, DDBDRAFT_0231397, DDBDRAFT_0231400, DDB_0205237, DDB_0231397, DDB_0231400, FH, Fh, Fh-1, Fh1, HLRCC, im:7152785, LRCC, MCL, MCUL1, ns:zf-e152, zf-e152, zgc:66253, zgc:77498Protein level used designations for FH
- fumarate hydratase, mitochondrial
- fumarate hydratase
- fumarase
- fumarate hydratase 1
- EF-3
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