(2 references)-
- 抗原 See all Lipase A (LIPA) 抗体
- Lipase A (LIPA) (Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA))
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适用
- 人
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宿主
- 小鼠
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克隆类型
- 单克隆
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标记
- This Lipase A antibody is un-conjugated
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应用范围
- ELISA
- 原理
- LAL Antibody
- 纯化方法
- Ascitic fluid
- 免疫原
- Purified recombinant fragment of LAL expressed in E. Coli.
- 克隆位点
- 9G7F12
- 亚型
- IgG2a
- Top Product
- Discover our top product LIPA Primary Antibody
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anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 1-399) antibody
LIPA 适用: 人 WB, ELISA, IP 宿主: 小鼠 Monoclonal 1F9 unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 22-399) antibodyLIPA 适用: 人 WB, ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (Center) antibodyLIPA 适用: 人, 小鼠 WB 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 1-399) antibodyLIPA 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 32-201) antibodyLIPA 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 32-358) antibodyLIPA 适用: 大鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 42-91) antibodyLIPA 适用: 人, 大鼠, 马, Pig, 猴 WB 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 1-399) antibodyLIPA 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (N-Term) antibodyLIPA 适用: 人, 大鼠, 马, Pig, Cow, 兔, 绵羊 WB 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) antibodyLIPA 适用: 人, 大鼠 WB 宿主: 兔 Polyclonal unconjugated
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- 应用备注
- ELISA: 1/10000
- 限制
- 仅限研究用
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- 状态
- Liquid
- 缓冲液
- Ascitic fluid containing 0.03 % sodium azide.
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- 4 °C,-20 °C
- 储存方法
- Store at 4°C short term. Aliquot and store at -20°C long term. Avoid freeze/thaw cycles.
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: "Severe chronic diarrhea and weight loss in cholesteryl ester storage disease: a case report." in: World journal of gastroenterology : WJG, Vol. 11, Issue 15, pp. 2364-6, (2005) (PubMed).
: "Wolman disease and cholesteryl ester storage disease diagnosed by histological and ultrastructural examination of intestinal and liver biopsy." in: Pathology, research and practice, Vol. 200, Issue 3, pp. 231-40, (2004) (PubMed).
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: "Severe chronic diarrhea and weight loss in cholesteryl ester storage disease: a case report." in: World journal of gastroenterology : WJG, Vol. 11, Issue 15, pp. 2364-6, (2005) (PubMed).
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- 抗原
- Lipase A (LIPA) (Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA))
- 别名
- LAL (LIPA 产品)
- 别名
- cesd antibody, lal antibody, LIPA antibody, CESD antibody, LAL antibody, Chole antibody, Chole2 antibody, Lip1 antibody, AA960673 antibody, Lal antibody, Lip-1 antibody, lipase A, lysosomal acid type antibody, lipase A, lysosomal acid, cholesterol esterase antibody, lipase A, lysosomal acid, cholesterol esterase L homeolog antibody, lysosomal acid lipase A antibody, LIPA antibody, lipa antibody, lipa.L antibody, Lipa antibody
- 背景
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Description: Lysosomal acid lipase (LAL), with 378-amino acid protein( 43-54 kDa), functions in the lysosome to catalyze the hydrolysis of cholesteryl esters and triglycerides which are taken up by receptor-mediated endocytosis. An inherited deficiency or low activity of human lysosomal acid lipase results in the intralysosomal storage of the respective lipid substrates. So it is also responsible for the rare conditions of Wolman disease and cholesteryl ester storage disease (CESD). As the enzyme is synthesized by all nucleated cells, lipid-laden cells are found in all organs, particularly in liver, spleen, the adrenal and the hemopoietic system, and in the intestine as well as in the lymph nodes, lungs, testes, and ovaries.
Aliases: LAL, CESD, LIPA
- 基因ID
- 3988
- HGNC
- 3988
- UniProt
- P38571
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