(2 references)-
- 抗原 See all Lipase A (LIPA) 抗体
- Lipase A (LIPA) (Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA))
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适用
- 人
- 宿主
- 请咨询
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克隆类型
- 单克隆
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标记
- This Lipase A antibody is un-conjugated
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应用范围
- Western Blotting (WB), ELISA
- 特异性
- Ni-NTA purified truncated recombinant LAL expressed in E. Coli strain BL21 (DE3)
- 纯化方法
- Antibodies are purified by protein A affinity chromatography
- 亚型
- IgG1
- Top Product
- Discover our top product LIPA Primary Antibody
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anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 1-399) antibody
LIPA 适用: 人 WB, ELISA, IP 宿主: 小鼠 Monoclonal 1F9 unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 22-399) antibodyLIPA 适用: 人 WB, ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (Center) antibodyLIPA 适用: 人, 小鼠 WB 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 1-399) antibodyLIPA 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 32-201) antibodyLIPA 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 32-358) antibodyLIPA 适用: 大鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 42-91) antibodyLIPA 适用: 人, 大鼠, 马, Pig, 猴 WB 宿主: 兔 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (AA 1-399) antibodyLIPA 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) antibodyLIPA 适用: 人 ELISA 宿主: 小鼠 Monoclonal 9G7F12 unconjugated
anti-Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA) (N-Term) antibodyLIPA 适用: 人, 大鼠, 马, Pig, Cow, 兔, 绵羊 WB 宿主: 兔 Polyclonal unconjugated
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- 应用备注
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Western Blot: Dilution 1: 200- 1: 1,000
ELISA: Propose dilution 1: 10,000.
Determining optimal working dilutions by titration test. - 限制
- 仅限研究用
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- 储存条件
- -20 °C
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: "Severe chronic diarrhea and weight loss in cholesteryl ester storage disease: a case report." in: World journal of gastroenterology : WJG, Vol. 11, Issue 15, pp. 2364-6, (2005) (PubMed).
: "Wolman disease and cholesteryl ester storage disease diagnosed by histological and ultrastructural examination of intestinal and liver biopsy." in: Pathology, research and practice, Vol. 200, Issue 3, pp. 231-40, (2004) (PubMed).
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: "Severe chronic diarrhea and weight loss in cholesteryl ester storage disease: a case report." in: World journal of gastroenterology : WJG, Vol. 11, Issue 15, pp. 2364-6, (2005) (PubMed).
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- 抗原
- Lipase A (LIPA) (Lipase A, Lysosomal Acid, Cholesterol Esterase (LIPA))
- 别名
- LAL (LIPA 产品)
- 别名
- cesd antibody, lal antibody, LIPA antibody, CESD antibody, LAL antibody, Chole antibody, Chole2 antibody, Lip1 antibody, AA960673 antibody, Lal antibody, Lip-1 antibody, lipase A, lysosomal acid type antibody, lipase A, lysosomal acid, cholesterol esterase antibody, lipase A, lysosomal acid, cholesterol esterase L homeolog antibody, lysosomal acid lipase A antibody, LIPA antibody, lipa antibody, lipa.L antibody, Lipa antibody
- 背景
- Lysosomal acid lipase (LAL), with 378-amino acid protein( 43-54 kDa), functions in the lysosome to catalyze the hydrolysis of cholesteryl esters and triglycerides which are taken up by receptor-mediated endocytosis. An inherited deficiency or low activity of human lysosomal acid lipase results in the intralysosomal storage of the respective lipid substrates. So it is also responsible for the rare conditions of Wolman disease and cholesteryl ester storage disease (CESD). As the enzyme is synthesized by all nucleated cells, lipid-laden cells are found in all organs, particularly in liver, spleen, the adrenal and the hemopoietic system, and in the intestine as well as in the lymph nodes, lungs, testes, and ovaries.
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