-
- 抗原 See all HPS1 抗体
- HPS1 (Hermansky-Pudlak Syndrome 1 (HPS1))
-
适用
- 人
-
宿主
- 小鼠
-
克隆类型
- 单克隆
-
标记
- This HPS1 antibody is un-conjugated
-
应用范围
- Western Blotting (WB), ELISA
- 纯化方法
- Ascitic fluid
- 免疫原
- Purified recombinant fragment of HPS1 expressed in E. Coli.
- 克隆位点
- 5G12G2
- 亚型
- IgG2a
- Top Product
- Discover our top product HPS1 Primary Antibody
-
-
- 应用备注
-
Western Bloting: 1/500 - 1/2000.
ELISA: Propose dilution 1/10000.
Not yet tested in other applications.
Determining optimal working dilutions by titration test. - 限制
- 仅限研究用
-
- 状态
- Liquid
- 储存液
- Sodium azide
- 注意事项
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- 4 °C
-
-
Hermansky-Pudlak syndrome with interstitial pneumonia without mutation of HSP1 gene." in: Internal medicine (Tokyo, Japan), Vol. 44, Issue 6, pp. 616-21, (2005) (PubMed).
: "Biogenesis of lysosome-related organelles complex 3 (BLOC-3): a complex containing the Hermansky-Pudlak syndrome (HPS) proteins HPS1 and HPS4." in: Proceedings of the National Academy of Sciences of the United States of America, Vol. 100, Issue 15, pp. 8770-5, (2003) (PubMed).
: "
-
Hermansky-Pudlak syndrome with interstitial pneumonia without mutation of HSP1 gene." in: Internal medicine (Tokyo, Japan), Vol. 44, Issue 6, pp. 616-21, (2005) (PubMed).
-
- 抗原
- HPS1 (Hermansky-Pudlak Syndrome 1 (HPS1))
- 别名
- HPS1 (HPS1 产品)
- 别名
- HPS antibody, HPS1 antibody, MGC123240 antibody, im:7143944 antibody, zgc:123240 antibody, 6030422N11Rik antibody, BB405864 antibody, Hps antibody, ep antibody, HPS1, biogenesis of lysosomal organelles complex 3 subunit 1 antibody, Hermansky-Pudlak syndrome 1 antibody, HPS1 antibody, hps1 antibody, Hps1 antibody
- 背景
-
Hermansky-Pudlak syndrome 1. This protein may play a role in organelle biogenesis associated with melanosomes, platelet dense granules, and lysosomes. The encoded protein is a component of three different protein complexes termed biogenesis of lysosome-related organelles complex (BLOC)-3, BLOC4, and BLOC5. Mutations in this gene are associated with Hermansky-Pudlak syndrome type 1. Multiple transcript variants encoding distinct isoforms have been identified for this gene, the full-length sequences of some of these have not been determined yet.
Synonyms: HPS, MGC5277, HPS1 - 基因ID
- 3257
-