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AGLU 抗体 (N-Term)
AGLU
适用: 人
WB, EIA, IHC (p)
宿主: 兔
Polyclonal
unconjugated
AGLU抗体详情
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抗原
See all AGLU 抗体
AGLU
(alpha-Glucosidase (AGLU))
抗原表位
AA 173-203, N-Term
适用
All reactivities for AGLU 抗体
人
宿主
All hosts for AGLU 抗体
兔
克隆类型
All clonalities for AGLU 抗体
多克隆
标记
All conjugates for AGLU 抗体
This AGLU antibody is un-conjugated
应用范围
All applications for AGLU 抗体
Western Blotting (WB), Enzyme Immunoassay (EIA), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p))
特异性
This antibody recognizes Human Alpha-glucosidase (N-term).
纯化方法
Protein A column, followed by peptide affinity purification
免疫原
conjugated synthetic peptide between 173-203 amino acids from the N-terminal region of Human Alpha-glucosidase Genename: GAA
亚型
Ig Fraction
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Discover our top product AGLU Primary Antibody
Alternatives
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使用细节
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应用备注
Optimal working dilution should be determined by the investigator.
限制
仅限研究用
贮存及处理
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状态
Liquid
浓度
0.25 mg/mL
缓冲液
PBS containing 0.09 % (W/V) Sodium Azide as preservative
储存液
Sodium azide
注意事项
This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
注意事项
Avoid repeated freezing and thawing.
储存条件
4 °C/-20 °C
储存方法
Store undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
AGLU目标详情
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抗原
AGLU
(alpha-Glucosidase (AGLU))
别名
alpha-Glucosidase (AGLU 产品 )
别名
MG antibody, MGA antibody, SPAC56F8.01 antibody, SPAC922.02c antibody, CG11909 antibody, CT33098 antibody, Dmel\\CG11909 antibody, GB19017 antibody, 6030407P20Rik antibody, maltase-glucoamylase antibody, alpha-glucosidase (predicted) antibody, alpha-glucosidase antibody, glucosidase, alpha, acid antibody, target of brain insulin antibody, sucrase-isomaltase antibody, MGAM antibody, SPAC30D11.01c antibody, LMOf2365_0194 antibody, SPAC1039.11c antibody, Gaa antibody, tobi antibody, SI antibody, Hbg3 antibody, Mgam antibody
背景
This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum. Three transcript variants encoding the same protein have been found for this gene.Synonyms: Acid maltase, Aglucosidase alfa, GAA, LYAG, Lysosomal alpha-glucosidase
分子量
105319 Da
基因ID
2548
NCBI登录号
NP_000143
途径
Cellular Glucan Metabolic Process
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