GLA 抗体 (AA 101-200)
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- 抗原 See all GLA 抗体
- GLA (Galactosidase, alpha (GLA))
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抗原表位
- AA 101-200
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适用
- 人, 小鼠, 大鼠
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This GLA antibody is un-conjugated
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应用范围
- Western Blotting (WB), ELISA, Flow Cytometry (FACS), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p)), Immunohistochemistry (Frozen Sections) (IHC (fro))
- 交叉反应
- 人, 小鼠, 大鼠
- 预测反应
- Dog,Cow,Pig,Rabbit
- 纯化方法
- Purified by Protein A.
- 免疫原
- KLH conjugated synthetic peptide derived from human Galactosidase alpha
- 亚型
- IgG
- Top Product
- Discover our top product GLA Primary Antibody
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anti-Galactosidase, alpha (GLA) (AA 81-429) antibody
GLA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) (AA 81-429) antibodyGLA 适用: 人 WB, IHC, IP, ICC 宿主: 小鼠 Monoclonal C6 unconjugated
anti-Galactosidase, alpha (GLA) antibodyKO Validated GLA 适用: 人 WB, IP, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) (AA 1-80) antibodyGLA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) (AA 147-371) antibodyGLA 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) (AA 1-429) antibodyGLA 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) (AA 83-112), (N-Term) antibodyGLA 适用: 人 WB, FACS, IF, IHC (p) 宿主: 兔 Polyclonal RB19115 unconjugated
anti-Galactosidase, alpha (GLA) (AA 32-429) antibodyGLA 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) (AA 1-429) antibodyGLA 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Galactosidase, alpha (GLA) (AA 150-429) antibodyGLA 适用: 人 WB, IF 宿主: 兔 Polyclonal unconjugated
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- 应用备注
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WB 1:300-5000
ELISA 1:500-1000
FCM 1:20-100
IHC-P 1:200-400
IHC-F 1:100-500
IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200 - 限制
- 仅限研究用
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- 状态
- Liquid
- 浓度
- 1 μg/μL
- 缓冲液
- 0.01M TBS( pH 7.4) with 1 % BSA, 0.02 % Proclin300 and 50 % Glycerol.
- 储存液
- ProClin
- 注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
- 储存条件
- 4 °C,-20 °C
- 储存方法
- Shipped at 4°C. Store at -20°C for one year. Avoid repeated freeze/thaw cycles.
- 有效期
- 12 months
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- 抗原
- GLA (Galactosidase, alpha (GLA))
- 别名
- Galactosidase alpha (GLA 产品)
- 别名
- GALA antibody, Ags antibody, zgc:101584 antibody, MGC130872 antibody, SMU.877 antibody, SCF11.21 antibody, AO090005000217 antibody, alpha-GAL antibody, galactosidase alpha antibody, galactosidase, alpha antibody, galactosidase alpha S homeolog antibody, alpha-galactosidase antibody, aga antibody, alpha-galactosidase A antibody, GLA antibody, Gla antibody, gla antibody, gla.S antibody, agaN antibody, aga antibody, agaL antibody, SCO0541 antibody, rafA antibody, melA antibody, galA antibody, ANI_1_2528074 antibody, ANI_1_1502124 antibody, AOR_1_390174 antibody, CpipJ_CPIJ002066 antibody, MCYG_00962 antibody, MCYG_00791 antibody, Tsp_02909 antibody, Tsp_02508 antibody
- 背景
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Synonyms: GALA, Alpha-galactosidase A, Alpha-D-galactosidase A, Alpha-D-galactoside galactohydrolase, Melibiase, GLA
Background: Galactosidase alpha is involved in the hydrolysis of terminal, non reducing alpha D galactose residues in alpha D galactosides, including galactose oligosaccharides, galactomannans and galactohydrolase. Defects in GLA are the cause of Fabry's disease (FD). FD is a rare X-linked sphingolipidosis disease where glycolipid accumulates in many tissues. Clinical recognition in males results from characteristic skin lesions (angiokeratomas) over the lower trunk. Patients may show ocular deposits, febrile episodes, and burning pain in the extremities. Death results from renal failure, cardiac or cerebral complications of hypertension or other vascular disease. Heterozygous females may exhibit the disorder in an attenuated form, they are more likely to show corneal opacities.
- 基因ID
- 2717
- UniProt
- P06280
- 途径
- SARS-CoV-2 Protein Interactome
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