The protein encoded by this gene is an enzyme that synthesizes the prenyl side-chain of coenzyme Q, or ubiquinone, one of the key elements in the respiratory chain. The gene product catalyzes the formation of all trans-polyprenyl pyrophosphates from isopentyl diphosphate in the assembly of polyisoprenoid side chains, the first step in coenzyme Q biosynthesis. Defects in this gene are a cause of coenzyme Q10 deficiency.,PDSS2,C6orf210,COQ10D3,DLP1,bA59I9.3,hDLP1,Cancer,Tumor suppressors,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,PDSS2