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GCH1 抗体

GCH1 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
产品编号 ABIN7190766
发货至: 中国
  • 抗原 See all GCH1 抗体
    GCH1 (GTP Cyclohydrolase 1 (GCH1))
    适用
    • 40
    • 24
    • 10
    • 4
    • 4
    • 4
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    宿主
    • 48
    • 7
    • 1
    克隆类型
    • 53
    • 3
    多克隆
    标记
    • 22
    • 5
    • 5
    • 3
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
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    This GCH1 antibody is un-conjugated
    应用范围
    • 47
    • 28
    • 17
    • 13
    • 13
    • 6
    • 5
    • 4
    • 3
    Western Blotting (WB), ELISA, Immunohistochemistry (IHC)
    交叉反应
    纯化方法
    Antigen affinity purification
    免疫原
    Synthetic peptide of Human GCH1
    亚型
    IgG
    Top Product
    Discover our top product GCH1 Primary Antibody
  • 应用备注
    ELISA:1:1000-1:2000, WB:1:200-1:1000, IHC:1:5-1:20,
    限制
    仅限研究用
  • 状态
    Liquid
    缓冲液
    -20 °C, pH 7.4 PBS, 0.05 % Sodium azide, 40 % Glycerol
    储存液
    Sodium azide
    注意事项
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    储存条件
    -20 °C,-80 °C
    储存方法
    Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
  • 抗原
    GCH1 (GTP Cyclohydrolase 1 (GCH1))
    别名
    GCH1 (GCH1 产品)
    别名
    DYT14 antibody, DYT5 antibody, DYT5a antibody, GCH antibody, GTP-CH-1 antibody, GTPCH1 antibody, HPABH4B antibody, GTP-CH antibody, GTPCH antibody, Gch antibody, MGC89622 antibody, gch1a antibody, wu:fc16b10 antibody, zgc:195269 antibody, GTP cyclohydrolase 1 antibody, GTP cyclohydrolase 1-like antibody, GCH1 antibody, Gch1 antibody, gch1 antibody, Weevi_1190 antibody, Halhy_0838 antibody, Sinme_1220 antibody, Sphch_1077 antibody, LOC100136794 antibody
    背景

    Background: This gene encodes a member of the GTP cyclohydrolase family. The encoded protein is the first and rate-limiting enzyme in tetrahydrobiopterin (BH4) biosynthesis, catalyzing the conversion of GTP into 7,8-dihydroneopterin triphosphate. BH4 is an essential cofactor required by aromatic amino acid hydroxylases as well as nitric oxide synthases. Mutations in this gene are associated with malignant hyperphenylalaninemia and dopa-responsive dystonia. Several alternatively spliced transcript variants encoding different isoforms have been described, however, not all variants give rise to a functional enzyme.

    Aliases: dystonia 14 antibody, DYT 5 antibody, DYT14 antibody, DYT5 antibody, DYT5a antibody, GCH 1 antibody, GCH antibody, Gch1 antibody, GCH1_HUMAN antibody, GTP CH 1 antibody, GTP CH I antibody, GTP cyclohydrolase 1 (dopa responsive dystonia) antibody, GTP cyclohydrolase 1 antibody, GTP cyclohydrolase I antibody, GTP-CH-I antibody, GTPCH 1 antibody, GTPCH1 antibody, Guanosine 5' triphosphate cyclohydrolase I antibody, HPABH4B antibody

    UniProt
    P30793
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