MMADHC 抗体 (AA 26-142) (Biotin)
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- 抗原 See all MMADHC 抗体
- MMADHC (Methylmalonic Aciduria (Cobalamin Deficiency) CblD Type, with Homocystinuria (MMADHC))
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抗原表位
- AA 26-142
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适用
- 人
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This MMADHC antibody is conjugated to Biotin
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应用范围
- ELISA
- 交叉反应
- 人
- 纯化方法
- >95%, Protein G purified
- 免疫原
- Recombinant Human Methylmalonic aciduria and homocystinuria type D protein, mitochondrial protein (26-142AA)
- 亚型
- IgG
- Top Product
- Discover our top product MMADHC Primary Antibody
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- 应用备注
- Optimal working dilution should be determined by the investigator.
- 限制
- 仅限研究用
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- 状态
- Liquid
- 缓冲液
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Preservative: 0.03 % Proclin 300
Constituents: 50 % Glycerol, 0.01M PBS, pH 7.4 - 储存液
- ProClin
- 注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- -20 °C,-80 °C
- 储存方法
- Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
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- 抗原
- MMADHC (Methylmalonic Aciduria (Cobalamin Deficiency) CblD Type, with Homocystinuria (MMADHC))
- 别名
- MMADHC (MMADHC 产品)
- 别名
- C2orf25 antibody, CL25022 antibody, cblD antibody, 2010311D03Rik antibody, AI314967 antibody, RGD1303272 antibody, methylmalonic aciduria and homocystinuria, cblD type antibody, methylmalonic aciduria (cobalamin deficiency) cblD type, with homocystinuria antibody, MMADHC antibody, Mmadhc antibody
- 背景
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Background: Involved in cobalamin metabolism (PubMed:18385497, PubMed:23415655, PubMed:24722857, PubMed:26364851). Plays a role in regulating the biosynthesis of two coenzymes, methylcobalamin and adenosylcobalamin (PubMed:18385497, PubMed:24722857). Plays a role in regulating the proportion of methylcobalamin and adenosylcobalamin (PubMed:23415655, PubMed:24722857). Promotes oxidation of cob(II)alamin bound to MMACHC (PubMed:26364851).
Aliases: C2orf25 antibody, cblD antibody, Chromosome 2 open reading frame 25 antibody, CL25022 antibody, Methylmalonic aciduria (cobalamin deficiency) cblD type, with homocystinuria antibody, Methylmalonic aciduria and homocystinuria type D protein antibody, methylmalonic aciduria and homocystinuria type D protein, mitochondrial antibody, mitochondrial antibody, MMAD_HUMAN antibody, Mmadhc antibody, Protein C2orf25, mitochondrial antibody
- UniProt
- Q9H3L0
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