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- 抗原 See all NPHP1 抗体
- NPHP1 (Nephronophthisis 1 (Juvenile) (NPHP1))
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适用
- 人, 小鼠, 大鼠
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This NPHP1 antibody is un-conjugated
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应用范围
- Western Blotting (WB), Immunofluorescence (IF)
- 产品特性
- Polyclonal Antibody
- 纯化方法
- Affinity purification
- 免疫原
- Recombinant fusion protein of human NPHP1 (NP_001121651.1).
- 亚型
- IgG
- Top Product
- Discover our top product NPHP1 Primary Antibody
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anti-Nephronophthisis 1 (Juvenile) (NPHP1) (AA 345-614) antibody
NPHP1 适用: 人 WB, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) (AA 1-121) antibodyNPHP1 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) (AA 1-109) antibodyNPHP1 适用: 人 ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) antibodyNPHP1 适用: 人, 小鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) antibodyNPHP1 适用: 人 WB 宿主: 兔 Monoclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) (AA 1-121) antibodyNPHP1 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) (AA 1-109) antibodyNPHP1 适用: 人 WB, ELISA, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-Nephronophthisis 1 (Juvenile) (NPHP1) antibody (FITC)NPHP1 适用: 人 WB, ELISA, IHC, IHC (p) 宿主: 兔 Polyclonal FITC
anti-Nephronophthisis 1 (Juvenile) (NPHP1) antibody (Biotin)NPHP1 适用: 人 WB, ELISA, IHC, IHC (p) 宿主: 兔 Polyclonal Biotin
anti-Nephronophthisis 1 (Juvenile) (NPHP1) antibody (HRP)NPHP1 适用: 人 WB, ELISA, IHC, IHC (p) 宿主: 兔 Polyclonal HRP
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- 应用备注
- WB 1:500-1:2000 IF 1:50-1:100
- 限制
- 仅限研究用
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- 状态
- Liquid
- 浓度
- 1 mg/mL
- 缓冲液
- PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- 抗原
- NPHP1 (Nephronophthisis 1 (Juvenile) (NPHP1))
- 别名
- NPHP1 (NPHP1 产品)
- 别名
- JBTS4 antibody, NPH1 antibody, SLSN1 antibody, nephrocystin-1 antibody, NPHP1 antibody, im:7162391 antibody, wu:fi59g07 antibody, zgc:152930 antibody, Nphp1 antibody, nephrocystin 1 antibody, nephronophthisis 1 (juvenile) homolog (human) antibody, nephronophthisis 1 (juvenile) L homeolog antibody, nephronophthisis 1 antibody, nephrocystin-1 antibody, NPHP1 antibody, Nphp1 antibody, nphp1.L antibody, nphp1 antibody, LOC100725987 antibody
- 背景
- This gene encodes a protein with src homology domain 3 (SH3) patterns. This protein interacts with Crk-associated substrate, and it appears to function in the control of cell division, as well as in cell-cell and cell-matrix adhesion signaling, likely as part of a multifunctional complex localized in actin- and microtubule-based structures. Mutations in this gene cause familial juvenile nephronophthisis type 1, a kidney disorder involving both tubules and glomeruli. Defects in this gene are also associated with Senior-Loken syndrome type 1, also referred to as juvenile nephronophthisis with Leber amaurosis, which is characterized by kidney and eye disease, and with Joubert syndrome type 4, which is characterized by cerebellar ataxia, oculomotor apraxia, psychomotor delay and neonatal breathing abnormalities, sometimes including retinal dystrophy and renal disease. Multiple transcript variants encoding different isoforms have been found for this gene.
- 分子量
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Observed_MW: 83 kDa
Calculated_MW: 69 kDa/77 kDa/83 kDa
- 基因ID
- 4867
- UniProt
- O15259
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