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GLA 抗体
GLA
适用: 人, 小鼠
IHC, IF
宿主: 兔
Polyclonal
unconjugated
GLA抗体详情
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抗原
See all GLA 抗体
GLA
(Galactosidase, alpha (GLA))
适用
All reactivities for GLA 抗体
人, 小鼠
宿主
All hosts for GLA 抗体
兔
克隆类型
All clonalities for GLA 抗体
多克隆
标记
All conjugates for GLA 抗体
This GLA antibody is un-conjugated
应用范围
All applications for GLA 抗体
Immunohistochemistry (IHC), Immunofluorescence (IF)
产品特性
Polyclonal Antibody
纯化方法
Affinity purification
免疫原
Recombinant fusion protein of human GLA (NP_000160.1).
亚型
IgG
Top Product
Discover our top product GLA Primary Antibody
Alternatives
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使用细节
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应用备注
IHC 1:50-1:200 IF 1:50-1:100
限制
仅限研究用
贮存及处理
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状态
Liquid
浓度
1 mg/mL
缓冲液
PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3
储存液
Sodium azide
注意事项
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
储存条件
-20 °C
储存方法
Store at -20°C. Avoid freeze / thaw cycles.
GLA目标详情
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抗原
GLA
(Galactosidase, alpha (GLA))
别名
GLA (GLA 产品 )
别名
GALA antibody, Ags antibody, zgc:101584 antibody, MGC130872 antibody, SMU.877 antibody, SCF11.21 antibody, AO090005000217 antibody, alpha-GAL antibody, galactosidase alpha antibody, galactosidase, alpha antibody, galactosidase alpha S homeolog antibody, alpha-galactosidase antibody, aga antibody, alpha-galactosidase A antibody, GLA antibody, Gla antibody, gla antibody, gla.S antibody, agaN antibody, aga antibody, agaL antibody, SCO0541 antibody, rafA antibody, melA antibody, galA antibody, ANI_1_2528074 antibody, ANI_1_1502124 antibody, AOR_1_390174 antibody, CpipJ_CPIJ002066 antibody, MCYG_00962 antibody, MCYG_00791 antibody, Tsp_02909 antibody, Tsp_02508 antibody
背景
This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.
基因ID
2717
UniProt
P06280
途径
SARS-CoV-2 Protein Interactome
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