SLC25A19 抗体
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- 抗原 See all SLC25A19 抗体
- SLC25A19 (Solute Carrier Family 25 (Mitochondrial Thiamine Pyrophosphate Carrier), Member 19 (SLC25A19))
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适用
- 人, 小鼠, 大鼠
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This SLC25A19 antibody is un-conjugated
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应用范围
- Western Blotting (WB), Immunofluorescence (IF)
- 产品特性
- Polyclonal Antibody
- 纯化方法
- Affinity purification
- 免疫原
- Recombinant fusion protein of human SLC25A19 (NP_068380.3).
- 亚型
- IgG
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- 应用备注
- WB 1:500-1:2000 IF 1:50-1:200
- 限制
- 仅限研究用
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- 状态
- Liquid
- 浓度
- 1 mg/mL
- 缓冲液
- PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- 抗原
- SLC25A19 (Solute Carrier Family 25 (Mitochondrial Thiamine Pyrophosphate Carrier), Member 19 (SLC25A19))
- 别名
- SLC25A19 (SLC25A19 产品)
- 别名
- zgc:111878 antibody, 2900089E13Rik antibody, DNC antibody, MUP1 antibody, TPC antibody, MCPHA antibody, THMD3 antibody, THMD4 antibody, solute carrier family 25 member 19 antibody, solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19 antibody, Slc25a19 antibody, slc25a19 antibody, SLC25A19 antibody
- 背景
- This gene encodes a mitochondrial protein that is a member of the solute carrier family. Although this protein was initially thought to be the mitochondrial deoxynucleotide carrier involved in the uptake of deoxynucleotides into the matrix of the mitochondria, further studies have demonstrated that this protein instead functions as the mitochondrial thiamine pyrophosphate carrier, which transports thiamine pyrophosphates into mitochondria. Mutations in this gene cause microcephaly, Amish type, a metabolic disease that results in severe congenital microcephaly, severe 2-ketoglutaric aciduria, and death within the first year. Multiple alternatively spliced variants, encoding the same protein, have been identified for this gene.
- 分子量
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Observed_MW: 36 kDa
Calculated_MW: 29 kDa/35 kDa
- 基因ID
- 60386
- UniProt
- Q9HC21
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