TIMM8A/DDP 抗体
Quick Overview for TIMM8A/DDP 抗体 (ABIN7246412)
抗原
See all TIMM8A/DDP (TIMM8A) 抗体适用
宿主
克隆类型
标记
应用范围
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产品特性
- Polyclonal Antibody
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纯化方法
- Antigen affinity purification
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免疫原
- Fusion protein of human TIMM8A
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亚型
- IgG
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anti-Translocase of Inner Mitochondrial Membrane 8A (TIMM8A) (AA 9-97) antibody
TIMM8A 适用: 人 WB, ELISA, IHC (p) 宿主: 小鼠 Monoclonal 2F11 unconjugated
anti-Translocase of Inner Mitochondrial Membrane 8A (TIMM8A) (AA 1-97) antibodyTIMM8A 适用: 人 WB, IF 宿主: 小鼠 Polyclonal unconjugated
anti-Translocase of Inner Mitochondrial Membrane 8A (TIMM8A) (AA 1-72) antibodyTIMM8A 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 1A12 unconjugated
anti-Translocase of Inner Mitochondrial Membrane 8A (TIMM8A) (AA 1-97) antibodyTIMM8A 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Translocase of Inner Mitochondrial Membrane 8A (TIMM8A) (AA 1-97) antibodyTIMM8A 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
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应用备注
- IHC 1:40-1:200, ELISA 1:5000-1:10000
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限制
- 仅限研究用
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状态
- Liquid
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浓度
- 0.84 mg/mL
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缓冲液
- PBS with 0.05 % Sodium azide and 40 % Glycerol, pH 7.4
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储存液
- Sodium azide
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注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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储存条件
- -20 °C
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储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- TIMM8A/DDP (TIMM8A) (Translocase of Inner Mitochondrial Membrane 8A (TIMM8A))
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别名
- TIMM8A
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背景
- This translocase is involved in the import and insertion of hydrophobic membrane proteins from the cytoplasm into the mitochondrial inner membrane. The gene is mutated in Mohr-Tranebjaerg syndrome/Deafness Dystonia Syndrome (MTS/DDS) and it is postulated that MTS/DDS is a mitochondrial disease caused by a defective mitochondrial protein import system. Defects in this gene also cause Jensen syndrome, an X-linked disease with opticoacoustic nerve atrophy and muscle weakness. This protein, along with TIMM13, forms a 70 kDa heterohexamer. Alternative splicing results in multiple transcript variants encoding distinct isoforms.
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UniProt
- O60220
抗原
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