TIMM8A/DDP 抗体
Our Local Distributor
北京 101111
Quick Overview for TIMM8A/DDP 抗体 (ABIN7246412)
抗原
See all TIMM8A/DDP (TIMM8A) 抗体适用
宿主
克隆类型
标记
应用范围
-
-
产品特性
- Polyclonal Antibody
-
纯化方法
- Antigen affinity purification
-
免疫原
- Fusion protein of human TIMM8A
-
亚型
- IgG
-
-
anti-Translocase of Inner Mitochondrial Membrane 8A (TIMM8A) (AA 9-97) antibody
TIMM8A 适用: 人 ELISA, WB, IHC (p) 宿主: 小鼠 Monoclonal 2F11 unconjugated
anti-Translocase of Inner Mitochondrial Membrane 8A (TIMM8A) (AA 1-97) antibodyTIMM8A 适用: 人 WB, IF 宿主: 小鼠 Polyclonal unconjugated
anti-Translocase of Inner Mitochondrial Membrane 8A (TIMM8A) (AA 1-72) antibodyTIMM8A 适用: 人 ELISA, WB 宿主: 小鼠 Monoclonal 1A12 unconjugated
anti-Translocase of Inner Mitochondrial Membrane 8A (TIMM8A) (AA 1-97) antibodyTIMM8A 适用: 人 ELISA, IHC 宿主: 兔 Polyclonal unconjugated
-
-
应用备注
- IHC 1:40-1:200, ELISA 1:5000-1:10000
-
限制
- 仅限研究用
-
-
-
状态
- Liquid
-
浓度
- 0.84 mg/mL
-
缓冲液
- PBS with 0.05 % Sodium azide and 40 % Glycerol, pH 7.4
-
储存液
- Sodium azide
-
注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
-
储存条件
- -20 °C
-
储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
-
-
- TIMM8A/DDP (TIMM8A) (Translocase of Inner Mitochondrial Membrane 8A (TIMM8A))
-
别名
- TIMM8A
-
背景
- This translocase is involved in the import and insertion of hydrophobic membrane proteins from the cytoplasm into the mitochondrial inner membrane. The gene is mutated in Mohr-Tranebjaerg syndrome/Deafness Dystonia Syndrome (MTS/DDS) and it is postulated that MTS/DDS is a mitochondrial disease caused by a defective mitochondrial protein import system. Defects in this gene also cause Jensen syndrome, an X-linked disease with opticoacoustic nerve atrophy and muscle weakness. This protein, along with TIMM13, forms a 70 kDa heterohexamer. Alternative splicing results in multiple transcript variants encoding distinct isoforms.
-
UniProt
- O60220
抗原
-
