MCFD2 抗体 (AA 1-100) (AbBy Fluor® 680)
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- 抗原 See all MCFD2 抗体
- MCFD2 (Multiple Coagulation Factor Deficiency 2 (MCFD2))
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抗原表位
- AA 1-100
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适用
- 大鼠, 小鼠
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This MCFD2 antibody is conjugated to AbBy Fluor® 680
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应用范围
- Western Blotting (WB), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p))
- 交叉反应
- 小鼠, 大鼠
- 纯化方法
- Purified by Protein A.
- 免疫原
- KLH conjugated synthetic peptide derived from mouse MCFD2
- 亚型
- IgG
- Top Product
- Discover our top product MCFD2 Primary Antibody
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- 应用备注
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IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200 - 限制
- 仅限研究用
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- 状态
- Liquid
- 浓度
- 1 μg/μL
- 缓冲液
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
- 储存液
- ProClin
- 注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
- 有效期
- 12 months
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- 抗原
- MCFD2 (Multiple Coagulation Factor Deficiency 2 (MCFD2))
- 别名
- MCFD2 (MCFD2 产品)
- 别名
- hm:zeh1186 antibody, wu:fc23b10 antibody, wu:fd50d08 antibody, zgc:103713 antibody, zgc:109915 antibody, MCFD2 antibody, DKFZp469B098 antibody, F5F8D antibody, F5F8D2 antibody, LMAN1IP antibody, SDNSF antibody, 1810021C21Rik antibody, F5f8d antibody, Lman1ip antibody, Sdnsf antibody, multiple coagulation factor deficiency 2 antibody, multiple coagulation factor deficiency 2 L homeolog antibody, MCFD2 antibody, mcfd2 antibody, mcfd2.L antibody, Mcfd2 antibody
- 背景
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Synonyms: 1810021C21Rik, DKFZp686G21263, F5F8D, LMAN1IP, MCFD 2, Mcfd2, MCFD2_MOUSE, Multiple coagulation factor deficiency protein 2, Neural stem cell derived neuronal survival protein, Neural stem cell-derived neuronal survival protein, SDNSF.
Background: This gene encodes a soluble luminal protein with two calmodulin-like EF-hand motifs at its C-terminus. This protein forms a complex with LAMN1 (lectin mannose binding protein 1, also known as ERGIC-53) that facilitates the transport of coagulation factors V (FV) and VIII (FVIII) from the endoplasmic reticulum to the Golgi apparatus via an endoplasmic reticulum Golgi intermediate compartment (ERGIC). Mutations in this gene cause combined deficiency of FV and FVIII (F5F8D), a rare autosomal recessive bleeding disorder characterized by mild to moderate bleeding and coordinate reduction in plasma FV and FVIII levels. This protein has also been shown to maintain stem cell potential in adult central nervous system and is a marker for testicular germ cell tumors. The 3' UTR of this gene contains a transposon-like human repeat element named 'THE 1'. A processed RNA pseudogene of this gene is on chromosome 6p22.1. Alternative splicing results in multiple transcript variants encoding distinct isoforms. [provided by RefSeq, Jun 2010]
- 基因ID
- 193813
- UniProt
- Q8K5B2
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