TIMM8A/DDP 抗体
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- 抗原 See all TIMM8A/DDP (TIMM8A) 抗体
- TIMM8A/DDP (TIMM8A) (Translocase of Inner Mitochondrial Membrane 8A (TIMM8A))
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适用
- 人, 小鼠
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This TIMM8A/DDP antibody is un-conjugated
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应用范围
- Western Blotting (WB)
- 纯化方法
- Affinity purification
- 免疫原
- Recombinant protein of human TIMM8A
- 亚型
- IgG
- Top Product
- Discover our top product TIMM8A Primary Antibody
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- 应用备注
- WB 1:500 - 1:2000
- 限制
- 仅限研究用
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- 浓度
- 1 mg/mL
- 缓冲液
- Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3.
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- 抗原
- TIMM8A/DDP (TIMM8A) (Translocase of Inner Mitochondrial Membrane 8A (TIMM8A))
- 别名
- TIMM8A (TIMM8A 产品)
- 别名
- TIMM8A antibody, ddp antibody, tim8a antibody, timm8a antibody, DDP antibody, DDP1 antibody, DFN1 antibody, MTS antibody, TIM8 antibody, im:6896085 antibody, zgc:100916 antibody, Ddp1 antibody, Timm8a antibody, DXHXS1274E antibody, Fci-12 antibody, Tim8a antibody, translocase of inner mitochondrial membrane 8 homolog A (yeast) antibody, translocase of inner mitochondrial membrane 8A antibody, translocase of inner mitochondrial membrane 8 homolog A1 (yeast) antibody, translocase of inner mitochondrial membrane 8A1 antibody, TIMM8A antibody, timm8a antibody, Timm8a1 antibody
- 背景
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Synonyms: DDP 1,DDP,DDP1,Deafness dystonia protein 1,Deafness/dystonia peptide,DFN 1,DFN1,MGC12262,Mitochondrial import inner membrane translocase subunit Tim8 A,MTS,TIM 8A,TIM8,TIM8A,TIM8A,TIMM 8A,timm8a,Translocase of inner mitochondrial membrane 8 homolog A,X linked deafness dystonia protein,X-linked deafness dystonia protein
Background: This translocase is involved in the import and insertion of hydrophobic membrane proteins from the cytoplasm into the mitochondrial inner membrane. The gene is mutated in Mohr-Tranebjaerg syndrome/Deafness Dystonia Syndrome (MTS/DDS) and it is postulated that MTS/DDS is a mitochondrial disease caused by a defective mitochondrial protein import system. Defects in this gene also cause Jensen syndrome, an X-linked disease with opticoacoustic nerve atrophy and muscle weakness. This protein, along with TIMM13, forms a 70 kDa heterohexamer. Alternative splicing results in multiple transcript variants encoding distinct isoforms.
- 分子量
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Observed_MW: 11kDa
Calculated_MW: 10kDa
- 基因ID
- 1678
- UniProt
- O60220
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