SGSH 抗体 (AA 273-502)
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- 抗原 See all SGSH 抗体
- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
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抗原表位
- AA 273-502
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适用
- 人
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This SGSH antibody is un-conjugated
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应用范围
- Western Blotting (WB)
- 序列
- DNGIPFPSGR TNLYWPGTAE PLLVSSPEHP KRWGQVSEAY VSLLDLTPTI LDWFSIPYPS YAIFGSKTIH LTGRSLLPAL EAEPLWATVF GSQSHHEVTM SYPMRSVQHR HFRLVHNLNF KMPFPIDQDF YVSPTFQDLL NRTTAGQPTG WYKDLRHYYY RARWELYDRS RDPHETQNLA TDPRFAQLLE MLRDQLAKWQ WETHDPWVCA PDGVLEEKLS PQCQPLHNEL
- 交叉反应
- 人, 小鼠, 大鼠
- 产品特性
- Polyclonal Antibodies
- 免疫原
- Recombinant fusion protein containing a sequence corresponding to amino acids 273-502 of human SGSH (NP_000190.1).
- 亚型
- IgG
- Top Product
- Discover our top product SGSH Primary Antibody
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- 应用备注
- WB,1:500 - 1:2000
- 说明
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HIGH QUALITY
- 限制
- 仅限研究用
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- 状态
- Liquid
- 缓冲液
- PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- 抗原
- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
- 别名
- SGSH (SGSH 产品)
- 别名
- HSS antibody, MPS3A antibody, SFMD antibody, 4632406A19Rik antibody, N-sulfoglucosamine sulfohydrolase antibody, N-sulfoglucosamine sulfohydrolase (sulfamidase) antibody, SGSH antibody, Sgsh antibody
- 背景
- This gene encodes one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with Sanfilippo syndrome A, one type of the lysosomal storage disease mucopolysaccaridosis III, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.,SGSH,HSS,MPS3A,SFMD,Signal Transduction,Cell Biology & Developmental Biology,Cytoskeleton,Neuroscience,Neurodegenerative Diseases,SGSH
- 分子量
- 56 kDa
- 基因ID
- 6448
- UniProt
- P51688
- 途径
- Glycosaminoglycan Metabolic Process
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