The product of this gene performs the final step in processing a specific class of nuclear-encoded proteins targeted to the mitochondrial matrix or inner membrane. This protein is primarily involved in the maturation of oxidative phosphorylation (OXPHOS)-related proteins. This gene may contribute to the functional effects of frataxin deficiency and the clinical manifestations of Friedreich ataxia.,MIPEP,COXPD31,HMIP,MIP,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,MIPEP