L2HGDH 抗体 (AA 1-220)
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- 抗原 See all L2HGDH 抗体
- L2HGDH (L-2-Hydroxyglutarate Dehydrogenase (L2HGDH))
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抗原表位
- AA 1-220
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适用
- 人
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This L2HGDH antibody is un-conjugated
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应用范围
- Western Blotting (WB)
- 序列
- MVPALRYLVG ACGRARGLFA GGSPGACGFA SGRPRPLCGG SRSASTSSFD IVIVGGGIVG LASARALILR HPSLSIGVLE KEKDLAVHQT GHNSGVIHSG IYYKPESLKA KLCVQGAALL YEYCQQKGIS YKQCGKLIVA VEQEEIPRLQ ALYEKGLQNG VPGLRLIQQE DIKKKEPYCR GLMAIDCPHT GIVDYRQVAL SFAQDFQEAG GSVLTNFEVK
- 交叉反应
- 人, 小鼠
- 产品特性
- Polyclonal Antibodies
- 免疫原
- Recombinant fusion protein containing a sequence corresponding to amino acids 1-220 of human L2HGDH (NP_079160.1).
- 亚型
- IgG
- Top Product
- Discover our top product L2HGDH Primary Antibody
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- 应用备注
- WB,1:500 - 1:2000
- 说明
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HIGH QUALITY
- 限制
- 仅限研究用
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- 状态
- Liquid
- 缓冲液
- PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- 抗原
- L2HGDH (L-2-Hydroxyglutarate Dehydrogenase (L2HGDH))
- 别名
- L2HGDH (L2HGDH 产品)
- 别名
- RGD1306250 antibody, C14orf160 antibody, BC016226 antibody, L-2-hydroxyglutarate dehydrogenase antibody, L2hgdh antibody, L2HGDH antibody
- 背景
- This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive neurometabolic disorder resulting in moderate to severe mental retardation.,L2HGDH,C14orf160,L2HGA,Signal Transduction,Cell Biology & Developmental Biology,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,L2HGDH
- 分子量
- 48 kDa/50 kDa
- 基因ID
- 79944
- UniProt
- Q9H9P8
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