FKRP 抗体 (AA 30-220)
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- 抗原 See all FKRP 抗体
- FKRP (Fukutin Related Protein (FKRP))
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抗原表位
- AA 30-220
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适用
- 人
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This FKRP antibody is un-conjugated
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应用范围
- Western Blotting (WB), Immunohistochemistry (IHC)
- 序列
- QPRNSRARGP RRASAAGPRV TVLVREFEAF DNAVPELVDS FLQQDPAQPV VVAADTLPYP PLALPRIPNV RLALLQPALD RPAAASRPET YVATEFVALV PDGARAEAPG LLERMVEALR AGSARLVAAP VATANPARCL ALNVSLREWT ARYGAAPAAP RCDALDGDAV VLLRARDLFN LSAPLARPVG T
- 交叉反应
- 人, 小鼠, 大鼠
- 产品特性
- Polyclonal Antibodies
- 纯化方法
- Affinity purification
- 免疫原
- Recombinant fusion protein containing a sequence corresponding to amino acids 30-220 of human FKRP (NP_077277.1).
- 亚型
- IgG
- Top Product
- Discover our top product FKRP Primary Antibody
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- 应用备注
- WB,1:1000 - 1:3000,IHC,1:50 - 1:200
- 说明
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HIGH QUALITY
- 限制
- 仅限研究用
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- 状态
- Liquid
- 缓冲液
- PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Avoid freeze / thaw cycles.
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- 抗原
- FKRP (Fukutin Related Protein (FKRP))
- 别名
- FKRP (FKRP 产品)
- 别名
- zgc:162829 antibody, LGMD2I antibody, MDC1C antibody, MDDGA5 antibody, MDDGB5 antibody, MDDGC5 antibody, A830029B19Rik antibody, AI842067 antibody, AI847300 antibody, LGMD1I antibody, fukutin related protein antibody, FKRP antibody, fkrp antibody, Fkrp antibody
- 背景
- This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined.,FKRP,LGMD2I,MDC1C,MDDGA5,MDDGB5,MDDGC5,Signal Transduction,FKRP
- 分子量
- 54 kDa
- 基因ID
- 79147
- UniProt
- Q9H9S5
- 途径
- Regulation of Carbohydrate Metabolic Process
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