Peroxisomal Bifunctional Enzyme 抗体 (Middle Region)
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- 抗原 See all Peroxisomal Bifunctional Enzyme (ECHP) products
- Peroxisomal Bifunctional Enzyme (ECHP)
- 抗原表位
- Middle Region
- 适用
- 人
- 宿主
- 兔
- 克隆类型
- 多克隆
- 应用范围
- Western Blotting (WB)
- 序列
- VIAVDSDKNQ LATANKMITS VLEKEASKMQ QSGHPWSGPK PRLTSSVKEL
- 产品特性
- This is a rabbit polyclonal antibody against ECHP. It was validated on Western Blot.
- 纯化方法
- Affinity purified
- 免疫原
- The immunogen is a synthetic peptide directed towards the middle region of Human ECHP
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- 应用备注
- Optimal working dilution should be determined by the investigator.
- 限制
- 仅限研究用
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- 状态
- Liquid
- 缓冲液
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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- 抗原
- Peroxisomal Bifunctional Enzyme (ECHP)
- 别名
- ECHP (ECHP 产品)
- 背景
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The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene.
Alias Symbols: EHHADH, ECHD,
Protein Size: 723 - 基因ID
- 1962
- NCBI登录号
- NP_001957
- UniProt
- Q08426
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