ETHE1 抗体 (AA 191-254) (AbBy Fluor® 594)
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- 抗原 See all ETHE1 抗体
- ETHE1 (Ethylmalonic Encephalopathy 1 (ETHE1))
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抗原表位
- AA 191-254
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适用
- 人
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This ETHE1 antibody is conjugated to AbBy Fluor® 594
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应用范围
- Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p))
- 预测反应
- Human,Mouse,Dog,Cow,Sheep,Pig,Rabbit
- 纯化方法
- Purified by Protein A.
- 免疫原
- KLH conjugated synthetic peptide derived from human E1
- 亚型
- IgG
- Top Product
- Discover our top product ETHE1 Primary Antibody
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anti-Ethylmalonic Encephalopathy 1 (ETHE1) (AA 8-245) antibody
ETHE1 适用: 人 WB, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Ethylmalonic Encephalopathy 1 (ETHE1) antibodyETHE1 适用: 人, 小鼠, 大鼠 WB, IHC, IF 宿主: 兔 Polyclonal unconjugated
anti-Ethylmalonic Encephalopathy 1 (ETHE1) (AA 1-254) antibodyETHE1 适用: 人 WB, IHC (p), IF 宿主: 小鼠 Polyclonal unconjugated
anti-Ethylmalonic Encephalopathy 1 (ETHE1) (AA 103-130) antibodyETHE1 适用: 人, 小鼠 WB, IHC (p), FACS 宿主: 兔 Polyclonal RB20157 unconjugated
anti-Ethylmalonic Encephalopathy 1 (ETHE1) (AA 8-254) antibodyETHE1 适用: 人 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Ethylmalonic Encephalopathy 1 (ETHE1) antibodyETHE1 适用: 人, 小鼠 WB, IHC, FACS 宿主: 兔 Polyclonal unconjugated
anti-Ethylmalonic Encephalopathy 1 (ETHE1) antibodyETHE1 适用: 人, 小鼠 WB, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Ethylmalonic Encephalopathy 1 (ETHE1) (AA 92-141) antibodyETHE1 适用: 人, 小鼠, 大鼠, Cow, 犬, 豚鼠, 马 WB 宿主: 兔 Polyclonal unconjugated
anti-Ethylmalonic Encephalopathy 1 (ETHE1) (AA 180-209) antibodyETHE1 适用: 人, 小鼠 WB, IHC, IHC (p) 宿主: 兔 Polyclonal unconjugated
anti-Ethylmalonic Encephalopathy 1 (ETHE1) (AA 180-209), (C-Term) antibodyETHE1 适用: 人, 小鼠 WB, IHC (p) 宿主: 兔 Polyclonal RB20158 unconjugated
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- 应用备注
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IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200 - 限制
- 仅限研究用
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- 状态
- Liquid
- 浓度
- 1 μg/μL
- 缓冲液
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
- 储存液
- ProClin
- 注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
- 有效期
- 12 months
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- 抗原
- ETHE1 (Ethylmalonic Encephalopathy 1 (ETHE1))
- 别名
- ETHE1 (ETHE1 产品)
- 别名
- zgc:85680 antibody, HSCO antibody, YF13H12 antibody, 0610025L15Rik antibody, Hsco antibody, ETHE1, persulfide dioxygenase antibody, ethylmalonic encephalopathy 1 antibody, Ethe1 antibody, ethe1 antibody, ETHE1 antibody
- 背景
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Synonyms: mitochondrial, Ethe1, ETHE1 protein, mitochondrial precursor, ETHE1_HUMAN, ethylmalonic encephalopathy 1, Ethylmalonic encephalopathy protein 1, hepatoma subtracted clone one, Hepatoma subtracted clone one protein, HSCO, Protein ETHE1, YF13H12.
Background: Probably plays an important role in metabolic homeostasis in mitochondria. May function as a nuclear-cytoplasmic shuttling protein that binds transcription factor RELA/NFKB3 in the nucleus and exports it to the cytoplasm. Suppresses p53-induced apoptosis by preventing nuclear localization of RELA.Involvement in disease:Defects in ETHE1 are a cause of ethylmalonic encephalopathy (EE) . EE is an autosomal recessive disorder characterized by neurodevelopmental delay and regression, recurrent petechiae, acrocyanosis, diarrhea, leading to death in the first decade of life. It is also associated with persistent lactic acidemia and ethylmalonic and methylsuccinic aciduria.
- 基因ID
- 23474
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