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GORAB 抗体 (AA 201-300) (AbBy Fluor® 594)

GORAB 适用: 人 WB, IF (cc), IF (p) 宿主: 兔 Polyclonal AbBy Fluor® 594
产品编号 ABIN2806237
发货至: 中国
  • 抗原 See all GORAB 抗体
    GORAB (Golgin, RAB6-Interacting (GORAB))
    抗原表位
    • 14
    • 9
    • 8
    • 6
    • 3
    • 3
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 201-300
    适用
    • 48
    • 18
    • 9
    • 1
    • 1
    宿主
    • 43
    • 5
    克隆类型
    • 45
    • 3
    多克隆
    标记
    • 21
    • 3
    • 3
    • 3
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    This GORAB antibody is conjugated to AbBy Fluor® 594
    应用范围
    • 41
    • 17
    • 12
    • 12
    • 7
    • 6
    • 5
    • 3
    • 2
    • 1
    • 1
    Western Blotting (WB), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p))
    交叉反应
    预测反应
    Mouse,Rat,Dog,Cow,Pig,Horse,Chicken,Rabbit
    纯化方法
    Purified by Protein A.
    免疫原
    KLH conjugated synthetic peptide derived from human SCYL1BP1
    亚型
    IgG
    Top Product
    Discover our top product GORAB Primary Antibody
  • 应用备注
    IF(IHC-P) 1:50-200
    IF(IHC-F) 1:50-200
    IF(ICC) 1:50-200
    限制
    仅限研究用
  • 状态
    Liquid
    浓度
    1 μg/μL
    缓冲液
    Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
    储存液
    ProClin
    注意事项
    This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
    储存条件
    -20 °C
    储存方法
    Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
    有效期
    12 months
  • 抗原
    GORAB (Golgin, RAB6-Interacting (GORAB))
    别名
    SCYL1BP1 (GORAB 产品)
    别名
    GO antibody, NTKLBP1 antibody, SCYL1BP1 antibody, AI467484 antibody, NTKL-BP1 antibody, Scyl1bp1 antibody, golgin, RAB6 interacting antibody, golgin, RAB6-interacting antibody, GORAB antibody, Gorab antibody
    背景

    Synonyms: GO, NTKLBP1, SCYL1BP1, RAB6-interacting golgin, N-terminal kinase-like-binding protein 1, NTKL-BP1, NTKL-binding protein 1, hNTKL-BP1, SCY1-like 1-binding protein 1, SCYL1-BP1, SCYL1-binding protein 1, GORAB

    Background: Defects in GORAB are the cause of geroderma osteodysplasticum (GO) [MIM:231070], also known as gerodermia osteodysplastica or Walt Disney dwarfism. GO is a rare autosomal recessive disorder characterized by lax, wrinkled skin, joint laxity and a typical face with a prematurely aged appearance. Skeletal signs include severe osteoporosis leading to frequent fractures, malar and mandibular hypoplasia and a variable degree of growth retardation.

    基因ID
    92344
    UniProt
    Q5T7V8
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