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- 抗原 See all BCKDHB 抗体
- BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
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抗原表位
- N-Term
- 适用
- 人, 大鼠, Cow, 犬, 马, Pig, 兔
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This BCKDHB antibody is un-conjugated
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应用范围
- Western Blotting (WB)
- 序列
- GFLHPAATVE DAAQRRQVAH FTFQPDPEPR EYGQTQKMNL FQSVTSALDN
- 预测反应
- Cow: 93%, Dog: 93%, Horse: 93%, Human: 100%, Pig: 86%, Rabbit: 93%, Rat: 79%
- 产品特性
- This is a rabbit polyclonal antibody against BCKDHB. It was validated on Western Blot.
- 纯化方法
- Affinity Purified
- 免疫原
- The immunogen is a synthetic peptide directed towards the N-terminal region of Human BCKDHB
- Top Product
- Discover our top product BCKDHB Primary Antibody
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anti-Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB) (AA 41-70), (N-Term) antibody
BCKDHB 适用: 人 WB, FACS, IF, IHC (p) 宿主: 兔 Polyclonal RB20925 unconjugated
anti-Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB) (AA 44-74), (N-Term) antibodyBCKDHB 适用: 人 WB, FACS, IF, IHC (p), EIA 宿主: 兔 Polyclonal unconjugated
anti-Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB) (AA 183-392) antibodyBCKDHB 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
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- 限制
- 仅限研究用
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- 状态
- Liquid
- 浓度
- 1 mg/mL
- 缓冲液
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 注意事项
- Avoid repeat freeze-thaw cycles.
- 储存条件
- -20 °C
- 储存方法
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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- 抗原
- BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))
- 别名
- BCKDHB (BCKDHB 产品)
- 别名
- zgc:158777 antibody, BCKDHB antibody, E1B antibody, dJ279A18.1 antibody, branched chain keto acid dehydrogenase E1, beta polypeptide antibody, branched chain keto acid dehydrogenase E1 subunit beta antibody, branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog antibody, branched chain ketoacid dehydrogenase E1, beta polypeptide antibody, BCKDHB antibody, bckdhb antibody, bckdhb.S antibody, Bckdhb antibody
- 背景
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Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. Alternative splicing at this locus results in transcript variants with different 3' non-coding regions, but encoding the same isoform.
Protein Interaction Partner: CUL3, BCKDHA,
Protein Size: 218 - 分子量
- 23 kDa
- 基因ID
- 594
- UniProt
- Q5T2J3
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