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HMBS 抗体 (N-Term)

Name: HMBS 抗体 (N-Term)
SKU: ABIN2785718
Availability: OutOfStock

HMBS 适用: 人, 小鼠, 大鼠, 兔, 犬, 马, 豚鼠, Cow, 斑马鱼, 绵羊 WB 宿主: 兔 Polyclonal unconjugated

WB Suggested Anti-HMBS Antibody Titration: 0. (HMBS 抗体 (N-Term))

1 image

(1 reference)

产品编号 ABIN2785718

发货至: 中国

Datasheet as PDF

抗原 See all HMBS 抗体

HMBS (Hydroxymethylbilane Synthase (HMBS))
抗原表位
8

5

2

2

1

1

1

1

1

1

1

1
N-Term
适用
60

35

35

4

3

3

3

2

2

2

2

1

1

1

1
人, 小鼠, 大鼠, 兔, 犬, 马, 豚鼠, Cow, 斑马鱼, 绵羊
宿主
54

5

1
兔
Compatible Secondaries
克隆类型
48

12
多克隆
标记
25

4

3

2

2

2

2

2

2

2

1

1

1

1

1

1

1

1

1

1

1

1

1

1
This HMBS antibody is un-conjugated
应用范围
38

13

10

8

7

5

4

4

4

1

1

1
Western Blotting (WB)

序列

MRVIRVGTRK SQLARIQTDS VVATLKASYP GLQFEIIAMS TTGDKILDTA

预测反应

Cow: 100%, Dog: 100%, Guinea Pig: 100%, Horse: 100%, Human: 100%, Mouse: 100%, Rabbit: 100%, Rat: 100%, Sheep: 100%, Zebrafish: 100%

产品特性

This is a rabbit polyclonal antibody against HMBS. It was validated on Western Blot using a cell lysate as a positive control.

纯化方法

Affinity Purified

免疫原

The immunogen is a synthetic peptide directed towards the N terminal region of human HMBS

Top Product

Discover our top product HMBS Primary Antibody
anti-Hydroxymethylbilane Synthase (HMBS) (AA 283-330) antibody
HMBS 适用: 人 WB, ELISA, IHC, IF 宿主: 兔 Polyclonal unconjugated

anti-Hydroxymethylbilane Synthase (HMBS) (AA 1-361) antibody
HMBS 适用: 人 WB, IF 宿主: 兔 Polyclonal unconjugated

anti-Hydroxymethylbilane Synthase (HMBS) (AA 1-361) antibody
HMBS 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 3E8 unconjugated

anti-Hydroxymethylbilane Synthase (HMBS) (AA 85-337) antibody
HMBS 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated

anti-Hydroxymethylbilane Synthase (HMBS) (Internal Region) antibody
HMBS 适用: 人, 小鼠, 大鼠 WB, ELISA, IHC, IF, ICC 宿主: 兔 Polyclonal unconjugated

anti-Hydroxymethylbilane Synthase (HMBS) (AA 160-173) antibody
Verified HMBS 适用: 人 WB, ELISA, IHC 宿主: 山羊 Polyclonal unconjugated

anti-Hydroxymethylbilane Synthase (HMBS) (AA 1-361) antibody
HMBS 适用: 人 WB 宿主: 兔 Polyclonal unconjugated

anti-Hydroxymethylbilane Synthase (HMBS) antibody
HMBS 适用: 人, 小鼠, 大鼠 WB, ELISA 宿主: 兔 Polyclonal unconjugated

anti-Hydroxymethylbilane Synthase (HMBS) (AA 146-195) antibody
HMBS 适用: 人, 兔, 豚鼠, 猴 WB 宿主: 兔 Polyclonal unconjugated

anti-Hydroxymethylbilane Synthase (HMBS) (N-Term) antibody
HMBS 适用: 人, 小鼠, 大鼠, 兔, 犬, 马, 豚鼠, Cow, 斑马鱼, Pig, 猴, 非洲爪蟾, Bat WB 宿主: 兔 Polyclonal unconjugated

应用备注

Optimal working dilutions should be determined experimentally by the investigator.

说明

Antigen size: 344 AA

限制

仅限研究用
状态

Liquid

浓度

Lot specific

缓冲液

Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

储存液

Sodium azide

注意事项

This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

注意事项

Avoid repeated freeze-thaw cycles.

储存条件

-20 °C

储存方法

For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
Kuo, Lee, Chuang, Huang: "Acute intermittent porphyria with peripheral neuropathy: a follow-up study after hematin treatment." in: Journal of the neurological sciences, Vol. 260, Issue 1-2, pp. 231-5, (2007) (PubMed).
抗原

HMBS (Hydroxymethylbilane Synthase (HMBS))

别名

HMBS (HMBS 产品)

别名

PBG-D antibody, PBGD antibody, PORC antibody, UPS antibody, URO-S antibody, hemC antibody, pbg-d antibody, pbgd antibody, ups antibody, SPAC806.01 antibody, DDBDRAFT_0186148 antibody, DDBDRAFT_0231417 antibody, DDB_0186148 antibody, DDB_0231417 antibody, Hmbs antibody, NV50236 antibody, T25658 antibody, Ups antibody, Uros1 antibody, hmbs antibody, zgc:64128 antibody, hmbsl antibody, id:ibd5004 antibody, im:7140060 antibody, zgc:110690 antibody, hydroxymethylbilane synthase antibody, hydroxymethylbilane synthase S homeolog antibody, hydroxymethylbilane synthase L homeolog antibody, hydroxymethylbilane synthase (predicted) antibody, Hydroxymethylbilane synthase antibody, hydroxymethylbilane synthase a antibody, hydroxymethylbilane synthase, b antibody, HMBS antibody, Hmbs antibody, hmbs antibody, hmbs.2.S antibody, hmbs.L antibody, CNC02250 antibody, hem3 antibody, hemC antibody, Trad_0335 antibody, Plabr_2100 antibody, Sgly_3113 antibody, SMLT_RS19660 antibody, PMI_RS16580 antibody, hmbsa antibody, hmbsb antibody

背景

HMBS is a member of the hydroxymethylbilane synthase superfamily. It is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria.This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described.
Alias Symbols: PBG-D, PBGD, UPS, PORC
Protein Interaction Partner: RANBP9, APP, UBC,
Protein Size: 344

分子量

38 kDa

基因ID

3145

NCBI登录号

NM_001024382, NP_001019553

UniProt

P08397