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- 抗原 See all FUCA1 抗体
- FUCA1 (Fucosidase, alpha-L- 1, Tissue (FUCA1))
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适用
- 人, 小鼠, 大鼠
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This FUCA1 antibody is un-conjugated
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应用范围
- Western Blotting (WB), ELISA
- 纯化方法
- Antibody is purified by peptide affinity chromatography method.
- 免疫原
- Antibody produced in rabbits immunized with a synthetic peptide corresponding a region of human FUCA1.
- Top Product
- Discover our top product FUCA1 Primary Antibody
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anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 185-447) antibody
FUCA1 适用: 小鼠 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 53-289) antibodyFUCA1 适用: 人 WB, IHC, IP, ICC 宿主: 兔 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 1-461) antibodyFUCA1 适用: 人 WB, IP 宿主: 兔 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) antibodyFUCA1 适用: 人, 小鼠 WB, ELISA, IHC 宿主: 兔 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 321-420) antibodyFUCA1 适用: 小鼠 WB, ELISA, IF (cc), IF (p), IHC (p), IHC (fro) 宿主: 兔 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 1-461) antibodyFUCA1 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 23-461) antibodyFUCA1 适用: 人 WB, ELISA 宿主: 小鼠 Monoclonal 1D4 unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 265-294) antibodyFUCA1 适用: 人 WB, FACS, IHC (p) 宿主: 兔 Polyclonal RB19323 unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) antibodyFUCA1 适用: 人 WB, IHC, FACS 宿主: 兔 Polyclonal unconjugated
anti-Fucosidase, alpha-L- 1, Tissue (FUCA1) (AA 18-452) antibodyFUCA1 适用: 小鼠 WB, ELISA 宿主: 兔 Polyclonal unconjugated
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- 应用备注
- FUCA1 antibody can be used for detection of FUCA1 by ELISA at 1:312500. FUCA1 antibody can be used for detection of FUCA1 by western blot at 1 μg/mL, and HRP conjugated secondary antibody should be diluted 1:50,000 - 100,000.
- 限制
- 仅限研究用
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- 状态
- Lyophilized
- 溶解方式
- Add 50 ?L of distilled water. Final antibody concentration is 1 mg/mL.
- 浓度
- 1 mg/mL
- 缓冲液
- Antibody is lyophilized in PBS buffer with 2 % sucrose.
- 注意事项
- As with any antibody avoid repeat freeze-thaw cycles.
- 储存条件
- 4 °C/-20 °C
- 储存方法
- For short periods of storage (days) store at 4 °C. For longer periods of storage, store FUCA1 antibody at -20 °C.
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- 抗原
- FUCA1 (Fucosidase, alpha-L- 1, Tissue (FUCA1))
- 别名
- FUCA1 (FUCA1 产品)
- 别名
- FUCA antibody, FUCA1 antibody, 0610006A03Rik antibody, 9530055J05Rik antibody, Afuc antibody, Fuca antibody, fuca antibody, fuca1 antibody, ATFUC1 antibody, F24D13.11 antibody, F24D13_11 antibody, alpha-L-fucosidase 1 antibody, wu:fb02a09 antibody, zgc:101116 antibody, alpha-L-fucosidase 1 antibody, fucosidase, alpha-L- 1, tissue antibody, alpha-L-fucosidase 1 L homeolog antibody, alpha-L-fucosidase 1, tandem duplicate 2 antibody, FUCA1 antibody, Fuca1 antibody, fuca1.L antibody, fuca1 antibody, FUC1 antibody, LOC9317020 antibody, LOC100285202 antibody, fuca1.2 antibody
- 背景
- Alpha-L-fucosidase (EC 3.2.1.51) is a lysosomal enzyme involved in the degradation of fucose-containing glycoproteins and glycolipids. At least 2 separate polymorphic alpha-L-fucosidases are recognized in man: that in tissues, FUCA1, which is deficient in fucosidosis, and that in plasma, FUCA2. Fucosidosis is an autosomal recessive lysosomal storage disease caused by defective alpha-L-fucosidase with accumulation of fucose in the tissues. Different phenotypes include clinical features such as neurologic deterioration, growth retardation, visceromegaly, and seizures in a severe early form, coarse facial features, angiokeratoma corporis diffusum, spasticity and delayed psychomotor development in a longer surviving form, and an unusual spondylometaphyseoepiphyseal dysplasia in yet another form.
- 分子量
- 54 kDa
- 基因ID
- 2517
- NCBI登录号
- NP_000138
- UniProt
- P04066
- 途径
- Glycosaminoglycan Metabolic Process
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