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- 抗原 See all HPS5 抗体
- HPS5 (Hermansky-Pudlak Syndrome 5 (HPS5))
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抗原表位
- AA 88-116, N-Term
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适用
- 人
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This HPS5 antibody is un-conjugated
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应用范围
- Western Blotting (WB)
- 纯化方法
- This antibody is purified through a protein A column, followed by peptide affinity purification.
- 免疫原
- This HPS5 antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 88-116 amino acids from the N-terminal region of human HPS5.
- 克隆位点
- RB42226
- 亚型
- Ig Fraction
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- 应用备注
- WB: 1:1000
- 限制
- 仅限研究用
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- 状态
- Liquid
- 缓冲液
- Purified polyclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.
- 储存液
- Sodium azide
- 注意事项
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- 储存条件
- 4 °C,-20 °C
- 有效期
- 6 months
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Improper trafficking of melanocyte-specific proteins in Hermansky-Pudlak syndrome type-5." in: The Journal of investigative dermatology, Vol. 127, Issue 6, pp. 1471-8, (2007) (PubMed).
: "Platelet alpha granules in BLOC-2 and BLOC-3 subtypes of Hermansky-Pudlak syndrome." in: Platelets, Vol. 18, Issue 2, pp. 150-7, (2007) (PubMed).
: "ATM and ATR substrate analysis reveals extensive protein networks responsive to DNA damage." in: Science (New York, N.Y.), Vol. 316, Issue 5828, pp. 1160-6, (2007) (PubMed).
: "Cellular, molecular and clinical characterization of patients with Hermansky-Pudlak syndrome type 5." in: Traffic (Copenhagen, Denmark), Vol. 5, Issue 9, pp. 711-22, (2004) (PubMed).
: "Characterization of BLOC-2, a complex containing the Hermansky-Pudlak syndrome proteins HPS3, HPS5 and HPS6." in: Traffic (Copenhagen, Denmark), Vol. 5, Issue 4, pp. 276-83, (2004) (PubMed).
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Improper trafficking of melanocyte-specific proteins in Hermansky-Pudlak syndrome type-5." in: The Journal of investigative dermatology, Vol. 127, Issue 6, pp. 1471-8, (2007) (PubMed).
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- 抗原
- HPS5 (Hermansky-Pudlak Syndrome 5 (HPS5))
- 别名
- HPS5 (HPS5 产品)
- 别名
- AIBP63 antibody, Aa2-028 antibody, Ab1-018 antibody, zgc:162420 antibody, AI646796 antibody, AL022647 antibody, C85120 antibody, haze antibody, hz antibody, maroon antibody, mr antibody, ru-2 antibody, ru2 antibody, HPS5, biogenesis of lysosomal organelles complex 2 subunit 2 antibody, Hermansky-Pudlak syndrome 5 antibody, HPS5 antibody, Hps5 antibody, hps5 antibody
- 背景
- This gene encodes a protein that may play a role in organelle biogenesis associated with melanosomes, platelet dense granules, and lysosomes. This protein interacts with Hermansky-Pudlak syndrome 6 protein and may interact with the cytoplasmic domain of integrin, alpha-3. Mutations in this gene are associated with Hermansky-Pudlak syndrome type 5. Multiple transcript variants encoding two distinct isoforms have been identified for this gene.
- 分子量
- 127449
- NCBI登录号
- NP_009147, NP_852608, NP_852609
- UniProt
- Q9UPZ3
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