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CTNS 抗体 (C-Term)

CTNS 适用: 人 WB 宿主: 兔 Polyclonal RB40519 unconjugated
产品编号 ABIN1881240
发货至: 中国
  • 抗原 See all CTNS 抗体
    CTNS (Cystinosis, Nephropathic (CTNS))
    抗原表位
    • 7
    • 6
    • 6
    • 3
    • 2
    • 1
    • 1
    • 1
    AA 341-367, C-Term
    适用
    • 25
    • 5
    • 5
    • 1
    • 1
    • 1
    • 1
    • 1
    宿主
    • 22
    • 3
    克隆类型
    • 23
    • 2
    多克隆
    标记
    • 15
    • 2
    • 2
    • 2
    • 2
    • 2
    This CTNS antibody is un-conjugated
    应用范围
    • 23
    • 18
    • 3
    • 3
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    Western Blotting (WB)
    纯化方法
    This antibody is purified through a protein A column, followed by peptide affinity purification.
    免疫原
    This CTNS antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 341-367 amino acids from the C-terminal region of human CTNS.
    克隆位点
    RB40519
    亚型
    Ig Fraction
    Top Product
    Discover our top product CTNS Primary Antibody
  • 应用备注
    WB: 1:1000
    限制
    仅限研究用
  • 状态
    Liquid
    缓冲液
    Purified polyclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.
    储存液
    Sodium azide
    注意事项
    This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    储存条件
    4 °C,-20 °C
    有效期
    6 months
  • Taranta, Wilmer, van den Heuvel, Bencivenga, Bellomo, Levtchenko, Emma: "Analysis of CTNS gene transcripts in nephropathic cystinosis." in: Pediatric nephrology (Berlin, Germany), Vol. 25, Issue 7, pp. 1263-7, (2010) (PubMed).

    Kumar, Bachhawat: "A futile cycle, formed between two ATP-dependant gamma-glutamyl cycle enzymes, gamma-glutamyl cysteine synthetase and 5-oxoprolinase: the cause of cellular ATP depletion in nephrotic cystinosis?" in: Journal of biosciences, Vol. 35, Issue 1, pp. 21-5, (2010) (PubMed).

    Bellomo, Corallini, Pastore, Palma, Laurenzi, Emma, Taranta: "Modulation of CTNS gene expression by intracellular thiols." in: Free radical biology & medicine, Vol. 48, Issue 7, pp. 865-72, (2010) (PubMed).

    Aldahmesh, Humeidan, Almojalli, Khan, Rajab, AL-Abbad, Meyer, Alkuraya: "Characterization of CTNS mutations in Arab patients with cystinosis." in: Ophthalmic genetics, Vol. 30, Issue 4, pp. 185-9, (2009) (PubMed).

    Macías-Vidal, Rodés, Hernández-Pérez, Vilaseca, Coll: "Analysis of the CTNS gene in 32 cystinosis patients from Spain." in: Clinical genetics, Vol. 76, Issue 5, pp. 486-9, (2009) (PubMed).

  • 抗原
    CTNS (Cystinosis, Nephropathic (CTNS))
    别名
    CTNS (CTNS 产品)
    别名
    CTNS-LSB antibody, PQLC4 antibody, AI195360 antibody, AW049661 antibody, zgc:110194 antibody, CTNS antibody, cystinosin, lysosomal cystine transporter antibody, cystinosis, nephropathic antibody, cystinosin, lysosomal cystine transporter L homeolog antibody, CTNS antibody, Ctns antibody, ctns antibody, ctns.L antibody
    背景
    This gene encodes a seven-transmembrane domain protein that functions to transport cystine out of lysosomes. Its activity is driven by the H+ electrochemical gradient of the lysosomal membrane. Mutations in this gene cause cystinosis, a lysosomal storage disorder. Alternative splicing results in multiple transcript variants.
    分子量
    41738
    NCBI登录号
    NP_001026851, NP_004928
    UniProt
    O60931
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