GNS 抗体 (AA 1-100)
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- 抗原 See all GNS 抗体
- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
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抗原表位
- AA 1-100
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适用
- 人
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This GNS antibody is un-conjugated
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应用范围
- ELISA, Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p)), Immunohistochemistry (Paraffin-embedded Sections) (IHC (p)), Immunohistochemistry (Frozen Sections) (IHC (fro)), Immunocytochemistry (ICC)
- 预测反应
- Human,Mouse,Rat,Cow,Horse,Rabbit
- 纯化方法
- Purified by Protein A.
- 免疫原
- KLH conjugated synthetic peptide derived from human GNS/Glucosamine 6 sulfatase
- 亚型
- IgG
- Top Product
- Discover our top product GNS Primary Antibody
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anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 293-552) antibody
GNS 适用: 人 WB, IHC, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 1-552) antibodyGNS 适用: 人 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 293-552) antibodyGNS 适用: 人 IHC, ELISA 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 283-313) antibodyGNS 适用: 人 WB, IHC (p), FACS 宿主: 兔 Polyclonal RB19341 unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (C-Term) antibodyGNS 适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 犬, 斑马鱼 WB, IHC 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) antibodyGNS 适用: 人 WB, IHC, FACS 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 1-552) antibodyGNS 适用: 人 WB 宿主: 小鼠 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 312-361) antibodyGNS 适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 犬, Bat, 猴 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (AA 398-447) antibodyGNS 适用: 人, 小鼠, 大鼠, Cow, 山羊, 豚鼠, 马, 兔, 斑马鱼, Bat, 猴 WB 宿主: 兔 Polyclonal unconjugated
anti-Glucosamine (N-Acetyl)-6-Sulfatase (GNS) (C-Term) antibodyGNS 适用: 人, 小鼠, 大鼠 WB 宿主: 兔 Polyclonal unconjugated
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- 应用备注
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ELISA 1:500-1000
IHC-P 1:200-400
IHC-F 1:100-500
IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200
ICC 1:100-500 - 限制
- 仅限研究用
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- 状态
- Liquid
- 浓度
- 1 μg/μL
- 缓冲液
- 0.01M TBS( pH 7.4) with 1 % BSA, 0.02 % Proclin300 and 50 % Glycerol.
- 储存液
- ProClin
- 注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
- 储存条件
- 4 °C,-20 °C
- 储存方法
- Shipped at 4°C. Store at -20°C for one year. Avoid repeated freeze/thaw cycles.
- 有效期
- 12 months
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- 抗原
- GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))
- 别名
- Glucosamine 6 sulfatase (GNS 产品)
- 别名
- G6S antibody, 2610016K11Rik antibody, AU042285 antibody, C87209 antibody, N28088 antibody, NV14559 antibody, N-acetylglucosamine-6-sulfatase antibody, zgc:114066 antibody, gns antibody, wu:fi20h10 antibody, zgc:55370 antibody, glucosamine (N-acetyl)-6-sulfatase antibody, glucosamine (N-acetyl)-6-sulfatase S homeolog antibody, glucosamine (N-acetyl)-6-sulfatase a antibody, N-acetylglucosamine-6-sulfatase antibody, glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID), b antibody, GNS antibody, Gns antibody, gns.S antibody, gns antibody, gnsa antibody, CpipJ_CPIJ000745 antibody, Sros_7372 antibody, VDBG_04409 antibody, Halhy_3165 antibody, gnsb antibody
- 背景
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Synonyms: 2610016K11Rik, AU042285, C87209, G6S, Glucosamine N-acetyl 6 sulfatase, Glucosamine 6 sulfatase, Glucosamine-6-sulfatase, GNS, GNS_HUMAN, MGC21274, N acetylglucosamine 6 sulfatase [Precursor], N-acetylglucosamine-6-sulfatase, N28088.
Background: GNS is a 552 amino acid lysosomal enzyme that hydrolyzes the 6-sulfate groups of the N-acetyl-D-glucosamine 6-sulfate units of keratan sulfate and heparan sulfate. A member of the sulfatase family, GNS assists in the catabolism of heparin, and binds calcium as a cofactor. GNS deficiency results in an autosomal recessive lysosomal storage disorder known as mucopolysaccharidosis type IIID (Sanfilippo D syndrome), which is characterized by mild somatic disease and severe degeneration of the central nervous system. Subject to post-translational internal peptidase cleavage, GNS is encoded by a gene mapping to human chromosome 12q14.2 and mouse chromosome 10 D2.
- 基因ID
- 2799
- 途径
- Glycosaminoglycan Metabolic Process
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