HIBCH 抗体 (AA 251-350) (AbBy Fluor® 647)
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- 抗原 See all HIBCH 抗体
- HIBCH (3-hydroxyisobutyryl-CoA Hydrolase (HIBCH))
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抗原表位
- AA 251-350
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适用
- 人
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This HIBCH antibody is conjugated to AbBy Fluor® 647
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应用范围
- Western Blotting (WB), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p))
- 预测反应
- Human
- 纯化方法
- Purified by Protein A.
- 免疫原
- KLH conjugated synthetic peptide derived from human HIBCH
- 亚型
- IgG
- Top Product
- Discover our top product HIBCH Primary Antibody
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anti-3-hydroxyisobutyryl-CoA Hydrolase (HIBCH) antibody
HIBCH 适用: 人, 犬 WB, IHC, FACS, IHC (p) 宿主: 小鼠 Monoclonal 3H5 unconjugated
anti-3-hydroxyisobutyryl-CoA Hydrolase (HIBCH) antibodyHIBCH 适用: 人, 大鼠, 犬 WB, IF, FACS 宿主: 小鼠 Monoclonal 1C7 unconjugated
anti-3-hydroxyisobutyryl-CoA Hydrolase (HIBCH) (AA 1-170) antibodyHIBCH 适用: 小鼠 WB, IHC, ICC, IP 宿主: 兔 Polyclonal unconjugated
anti-3-hydroxyisobutyryl-CoA Hydrolase (HIBCH) (AA 33-330) antibodyHIBCH 适用: 人 WB, IF 宿主: 兔 Polyclonal unconjugated
anti-3-hydroxyisobutyryl-CoA Hydrolase (HIBCH) antibodyHIBCH 适用: 人, 大鼠, 犬 WB, IF, FACS 宿主: 小鼠 Monoclonal 5C5 unconjugated
anti-3-hydroxyisobutyryl-CoA Hydrolase (HIBCH) antibodyHIBCH 适用: 人, 大鼠, 犬, 猴 WB, IF, FACS 宿主: 小鼠 Monoclonal 3D11 unconjugated
anti-3-hydroxyisobutyryl-CoA Hydrolase (HIBCH) antibodyHIBCH 适用: 人, 大鼠, 犬, 猴 WB, IF, FACS 宿主: 小鼠 Monoclonal 4G1 unconjugated
anti-3-hydroxyisobutyryl-CoA Hydrolase (HIBCH) (AA 183-209) antibodyHIBCH 适用: 人 WB, IHC (p) 宿主: 兔 Polyclonal RB18227 unconjugated
anti-3-hydroxyisobutyryl-CoA Hydrolase (HIBCH) (Middle Region) antibodyHIBCH 适用: 人 WB, EIA 宿主: 兔 Polyclonal unconjugated
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- 应用备注
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IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200 - 限制
- 仅限研究用
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- 状态
- Liquid
- 浓度
- 1 μg/μL
- 缓冲液
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
- 储存液
- ProClin
- 注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
- 有效期
- 12 months
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- 抗原
- HIBCH (3-hydroxyisobutyryl-CoA Hydrolase (HIBCH))
- 别名
- Hibch (HIBCH 产品)
- 别名
- DDBDRAFT_0189353 antibody, DDBDRAFT_0233831 antibody, DDB_0189353 antibody, DDB_0233831 antibody, T11J7.4 antibody, T11J7_4 antibody, T11J7.5 antibody, T11J7_5 antibody, HIBYLCOAH antibody, 2610509I15Rik antibody, AI648812 antibody, zgc:110824 antibody, 3-hydroxyisobutyryl-coenzyme A hydrolase antibody, 3-hydroxyisobutyryl-coenzyme a hydrolase,putative antibody, 3-hydroxyisobutyryl-Coenzyme A hydrolase antibody, 3-hydroxyisobutyryl-CoA hydrolase (predicted) antibody, 3-hydroxyisobutyryl-CoA hydrolase antibody, ATP-dependent caseinolytic (Clp) protease/crotonase family protein antibody, putative 3-hydroxyisobutyryl-coenzyme A hydrolase antibody, 3-hydroxyisobutyryl-CoA hydrolase L homeolog antibody, PVX_100950 antibody, CpipJ_CPIJ012030 antibody, PKH_145800 antibody, hibch antibody, MCYG_05070 antibody, SPBC2D10.09 antibody, CNA02940 antibody, LACBIDRAFT_292320 antibody, SJAG_00944 antibody, VDBG_07520 antibody, AT2G30650 antibody, AT2G30660 antibody, LBRM_32_3920 antibody, HIBCH antibody, Hibch antibody, hibch.L antibody
- 背景
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Synonyms: 3 hydroxyisobutyryl Coenzyme A hydrolase, 3 hydroxyisobutyryl Coenzyme A hydrolase, mitochondrial, 3-hydroxyisobutyryl-CoA hydrolase, 3-hydroxyisobutyryl-coenzyme A hydrolase, BETA HYDROXYISOBUTYRYL COENZYME A HYDROLASE, HIB CoA hydrolase, HIB-CoA hydrolase, HIBCH, HIBCH_HUMAN, HIBCoA hydrolase, HIBYL CoA H, HIBYL CoAH, HIBYL-CoA-H, HIBYLCoA H, HIBYLCoAH, mitochondrial, HIBCH_HUMAN.
Background: HIBCH is a 386 amino acid protein belonging to the enoyl-CoA hydratase/isomerase family. Localizing to the mitochondria, HIBCH is highly expressed in liver and kidney, with lower levels found in heart, muscle and brain. HIBCH hydrolyzes HIBYL-CoA, a saline catabolite, and _-hydroxypropionyl-CoA, an intermediate in the minor pathway involved in the metabolism of proprionate. Existing as two alternatively spliced isoforms, the gene encoding HIBCH maps to human chromosome 2q32.2. Defects to this gene result in HIBCH deficiency (HIBCHD), known alternatively as deficiency of _-hydroxyisobutyryl CoA deacylase or methacrylic aciduria. HIBCHD is characterized by the accumulation of methacrylyl-CoA, a highly reactive compound that undergoes addition reactions with free sulfhydryl groups. Phenotypic symptoms include early deterioration of neurological function, delayed motor skill development and hypotonia.
- 基因ID
- 26275
- 途径
- Monocarboxylic Acid Catabolic Process
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