BPGM 抗体 (AbBy Fluor® 488)
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- 抗原 See all BPGM 抗体
- BPGM (2,3-bisphosphoglycerate Mutase (BPGM))
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适用
- 人, 小鼠, 大鼠
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This BPGM antibody is conjugated to AbBy Fluor® 488
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应用范围
- Western Blotting (WB), Flow Cytometry (FACS), Immunofluorescence (Paraffin-embedded Sections) (IF (p))
- 交叉反应
- 人, 小鼠, 大鼠
- 纯化方法
- Purified by Protein A.
- 免疫原
- KLH conjugated synthetic peptide derived from human BPGM
- 亚型
- IgG
- Top Product
- Discover our top product BPGM Primary Antibody
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- 应用备注
- IF(IHC-P) 1:50-200
- 限制
- 仅限研究用
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- 状态
- Liquid
- 浓度
- 1 μg/μL
- 缓冲液
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
- 储存液
- ProClin
- 注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
- 有效期
- 12 months
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- 抗原
- BPGM (2,3-bisphosphoglycerate Mutase (BPGM))
- 别名
- BPGM (BPGM 产品)
- 别名
- DPGM antibody, AI323730 antibody, AL022789 antibody, C86192 antibody, Ab2-098 antibody, zgc:92230 antibody, Bisphosphoglycerate mutase antibody, bisphosphoglycerate mutase antibody, 2,3-bisphosphoglycerate mutase antibody, bisphosphoglycerate mutase S homeolog antibody, pmge antibody, BPGM antibody, Bpgm antibody, bpgm antibody, bpgm.S antibody
- 背景
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Synonyms: 2,3-bisphosphoglycerate mutase, 2,3-bisphosphoglycerate synthase, 3-bisphosphoglycerate mutase, 3-bisphosphoglycerate synthase, 3-diphosphoglycerate mutase, Ab2 098, AI323730, AL022789, Bisphosphoglycerate mutase, BPG dependent PGAM, BPG-dependent PGAM , Bpgm, BPGM, C86192, DPGM, Erythrocyte 2,3 bisphosphoglycerate mutase, PMGE_HUMAN, 2,3-bisphosphoglycerate mutase, erythrocyte, erythrocyte, 2 antibody.
Background: BPGM (2,3-bisphosphoglycerate mutase) is a 259 amino acid protein that belongs to the phosphoglycerate mutase family and exists as a homodimer that plays a crucial role in the regulation of hemoglobin oxygen. Specifically, BPGM catalyzes the conversion of 3-D-glyceroyl phosphate to 2,3-bisD-glycerate (2,3-BPG), a reaction that is essential for controlling the concentration of 2,3-BPG within the cell. The gene encoding BPGM maps to human chromosome 7, which houses over 1,000 genes and comprises nearly 5 % of the human genome. Defects in some of the genes localized to chromosome 7 have been linked to Osteogenesis imperfecta, Williams-Beuren syndrome, Pendred syndrome, Lissencephaly, Citrullinemia and Shwachman-Diamond syndrome. Involvement in disease:Defects in BPGM are the cause of bisphosphoglycerate mutase deficiency (BPGMD) . A disease characterized by hemolytic anemia, splenomegaly, cholelithiasis and cholecystitis.
- 基因ID
- 669
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