RPGRIP1L 抗体 (AA 41-140) (AbBy Fluor® 647)
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- 抗原 See all RPGRIP1L 抗体
- RPGRIP1L (RPGRIP1-Like (RPGRIP1L))
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抗原表位
- AA 41-140
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适用
- 人
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宿主
- 兔
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克隆类型
- 多克隆
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标记
- This RPGRIP1L antibody is conjugated to AbBy Fluor® 647
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应用范围
- Western Blotting (WB), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p))
- 预测反应
- Human,Mouse,Rat,Dog,Cow,Sheep,Pig,Horse,Rabbit,Guinea Pig
- 纯化方法
- Purified by Protein A.
- 免疫原
- KLH conjugated synthetic peptide derived from human RPGRIP1L
- 亚型
- IgG
- Top Product
- Discover our top product RPGRIP1L Primary Antibody
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- 应用备注
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IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200 - 限制
- 仅限研究用
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- 状态
- Liquid
- 浓度
- 1 μg/μL
- 缓冲液
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
- 储存液
- ProClin
- 注意事项
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
- 储存条件
- -20 °C
- 储存方法
- Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
- 有效期
- 12 months
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- 抗原
- RPGRIP1L (RPGRIP1-Like (RPGRIP1L))
- 别名
- RPGRIP1L (RPGRIP1L 产品)
- 别名
- si:ch1073-301i20.1 antibody, mks5 antibody, cors3 antibody, jbts7 antibody, nphp8 antibody, CORS3 antibody, FTM antibody, JBTS7 antibody, MKS5 antibody, NPHP8 antibody, 1700047E16Rik antibody, 4931437C01 antibody, Ftm antibody, Nphp8 antibody, RGD1311099 antibody, RPGRIP1 like antibody, RPGRIP1-like antibody, Protein fantom antibody, Rpgrip1-like antibody, RPGRIP1L antibody, rpgrip1l antibody, mks-5 antibody, Rpgrip1l antibody
- 背景
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Synonyms: CORS 3, CORS3, Fantom, FTM, JBTS 1, JBTS 7, JBTS1, JBTS7, Joubert syndrome 1, Joubert syndrome 7, Meckel syndrome, type 1, RPGRIP1-like, Meckel syndrome, type 5, MKS 5, MKS5, NPHP 8, NPHP8, nephrocystin 8, Protein fantom, Retinitis pigmentosa GTPase regulator interacting protein 1 like, RPGR interacting protein 1 like protein, RPGRIP1 like protein, FTM_HUMAN.
Background: RPGRIP1L is a 1,315 amino acid protein that belongs to the RPGRIP1 family and is thought to function in programmed cell death, craniofacial development and formation of the left-right axis. Existing as two alternatively spliced isoforms that localize to the cytoplasm, cytoskeleton, centrosome and cilium basal body, RPGRIP1L interacts with nephrocystin-4 and is moderately expressed in brain, retina and kidney. Containing two C2 domains, RPGRIP1L is encoded by a gene that maps to human chromosome 16q12.2. Defects in the gene encoding RPGRIP1L are the cause of Joubert syndrome type 7 (JBTS7), COACH syndrome (COACHS) and Meckel syndrome type 5 (MKS5).
- 途径
- DNA Replication, Regulation of G-Protein Coupled Receptor Protein Signaling, Synthesis of DNA
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