Hexosaminidase A 抗体
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- 抗原 See all Hexosaminidase A (HEXA) 抗体
- Hexosaminidase A (HEXA)
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适用
- 人
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宿主
- 小鼠
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克隆类型
- 单克隆
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标记
- This Hexosaminidase A antibody is un-conjugated
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应用范围
- Western Blotting (WB), Flow Cytometry (FACS), Enzyme Immunoassay (EIA)
- 特异性
- Recognizes Beta-hexosaminidase alpha / HEXA
- 交叉反应 (详细)
- Species reactivity (tested):Human.
- 纯化方法
- Purified
- 克隆位点
- 3F10
- 亚型
- IgG2b
- Top Product
- Discover our top product HEXA Primary Antibody
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- 应用备注
- Optimal working dilution should be determined by the investigator.
- 限制
- 仅限研究用
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- 状态
- Liquid
- 浓度
- 1.0 mg/mL
- 缓冲液
- PBS, 0.05 % Sodium Azide, 0.5 % protein stabilizer
- 储存液
- Sodium azide
- 注意事项
- This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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- 抗原
- Hexosaminidase A (HEXA)
- 别名
- beta-Hexosaminidase alpha / HEXA (HEXA 产品)
- 别名
- TSD antibody, fc04h11 antibody, wu:fc04h11 antibody, wu:fv09f06 antibody, si:dkey-35i22.2 antibody, HEXA antibody, Hex-1 antibody, zgc:112084 antibody, hexosaminidase subunit alpha antibody, hexosaminidase B (beta polypeptide) antibody, CUGBP Elav-like family member 6 antibody, hexosaminidase A antibody, hexosaminidase A (alpha polypeptide) antibody, beta-hexosaminidase subunit alpha-like antibody, HEXA antibody, hexb antibody, CELF6 antibody, Hexa antibody, hexa antibody, LOC100228061 antibody
- 背景
- This gene encodes the alpha subunit of the lysosomal enzyme beta-hexosaminidase that, together with the cofactor GM2 activator protein, catalyzes the degradation of the ganglioside GM2, and other molecules containing terminal N-acetyl hexosamines. Beta-hexosaminidase is composed of two subunits, alpha and beta, which are encoded by separate genes. Both beta-hexosaminidase alpha and beta subunits are members of family 20 of glycosyl hydrolases. Mutations in the alpha or beta subunit genes lead to an accumulation of GM2 ganglioside in neurons and neurodegenerative disorders termed the GM2 gangliosidoses. Alpha subunit gene mutations lead to Tay-Sachs disease (GM2-gangliosidosis type I).Synonyms: Beta-N-acetylhexosaminidase subunit alpha, N-acetyl-beta-glucosaminidase subunit alpha
- 分子量
- 60.7 kDa
- 基因ID
- 3073
- 途径
- Sensory Perception of Sound, Glycosaminoglycan Metabolic Process
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